Oğuzhan OKUTAN, Tayfun ÇALIŞKAN, Harun UGAN, Murat APAYDIN, Dilaver TAŞ, Hatice KAYA, Ersin DEMİRER

İzole tek taraflı pulmoner arter yokluğu: Olgu sunumu

İzole tek taraflı pulmoner arter yokluğu nadir görülür. Anomali, aynı taraf altıncı aortik arkın gelişme eksikliğinden kaynaklanır. Hastalık uzun süre asemptomatik kalabildiği için, tanısında gecikme olabilmektedir. Bu anomali postero-anteriyor akciğer grafisinde hiperlüsent akciğer görünümüne neden olur. Klinik ve radyolojik olarak başka hastalıklar (Swyer-James-MacLeod sendromu, interstisyel akciğer hastalığı vs.) ile karışabilir. Bu yazıda, hastalığı uzun süre asemptomatik seyreden, ancak son bir aydır halsizlik, iştahsızlık, nefes darlığı ve balgamla karışık kan gelmesi yakınması ile kliniğimize başvuran 21 yaşında erkek hasta sunuldu. Hastaya toraks manyetik rezonans anjiyografik inceleme ile sağ tek taraflı pulmoner arter yokluğu tanısı kondu.

Isolated unilateral absence of pulmonary artery: A case report

Isolated unilateral absence of pulmonary artery is seen rarely. This anomaly arises from the absence of development of ipsilateral sixth aortic arch. Since this disease can remain asymptomatic for a long period, the diagnosis may be delayed. Hyperlucent hemitorax is seen in postero-anterior chest radigraph of patients with this anomaly. Unilateral absence of pulmonary artery can be confused with other diseases (such as Swyer-James-MacLeod syndrome, interstitial lung disease). In this article, a 21-year-old male patient with the absence of right pulmonary artery. He was presented with fatigue, loss of appetite, dyspnea and hemoptysis which had started one month before. The case was diagnosed to have left pulmonary artery only (i.e., absence of right pulmonary artery) by magnetic resonance angiography.

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