İlker ERTUĞRUL, Şeyma KAYALI, Tamer YOLDAŞ, Selmin KARADEMİR, Vehbi DOĞAN, Utku Arman ÖRÜN

Çocuklukta apikal hipertrofik kardiyomiyopati: çok nadir bir değişken

Apikal hipertrofik kardiyomiyopati klasik olarak sol ventrikülün apeksini tutan nadir bir hipertrofik kardiyomiyopati kardiyomiyopati rastlantısal bir bulgu olabilir ya da hastalar göğüs ağrısı, çarpıntı, dispne ve senkop ile başvurabilir. Bu yazıda asemptomatik olan, kardiyak değerlendirme için başvuran ve hipertrofik kardiyomiyopatinin apikal bir değişkeni olduğu tespit edilen yedi yaşında bir kızın klinik görünümü tanımlandı.

Apical hypertrophic cardiomyopathy in childhood: a very rare variant

Apical hypertrophic cardiomyopathy is a rare form of hypertrophic cardiomyopathy which classically involves the apex of the left ventricle. Apical hypertrophic cardiomyopathy can be an incidental finding, or patients may present with chest pain, palpitations, dyspnea, and syncope. In this article, we describe the clinical presentation of a seven-year-old girl who was asymptomatic, presented for cardiac evaluation and was detected to have an apical variant of hypertrophic cardiomyopathy.

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