Özgür PİRGON, Mehmet Emre ATABEK, Musa SİLAHLI, Ahmet SERT

Pachydermoperiostosis: İki vaka takdimi

Pachydermoperiostosis çocukluk çağında ender görülen, otozomal dominant kalıtılan, idiyopatik hipertrofik osteartropatiyi tanımlamak için kullanılır. Biz çocukluk çağında ender görülmesi nedeniyle ve eşlik edebilecek olan diğer özellikleri yönünden dikkati çekmek için farklı şikâyetlerle başvuran iki vaka sunuyoruz.

Anahtar Kelimeler:

Çocuk, Osteoartropati, primer hipertropik

Pachydermoperiostosis: Two case reports

Pachydermoperiostosis inherited autosomal dominantly, is a rare condition that describes idiopathic hypertrophic osteoarthropaty in childhood. We present two cases who appliealy with similar complaints to our department in order to draw attention to different complaints in these two cases.

Keywords:

Child, Osteoarthropathy, Primary Hypertrophic,

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