Rıza Doğan, Ulaş Kumbasar, Benan Bayrakçı, Serkan Uysal, Selman Kesici

Sternal kleft malformasyonunun cerrahi onarımı

Sternal kleft, embriyolojik gelişimin başlarında sternal füzyonun başarısızlığından kaynaklanan, nadir görülen, doğumsal bir göğüs duvarı malformasyonudur. Cerrahi düzeltme hem mediastinal yapıları korumak hem de solunum dinamiklerini yeniden sağlamak için tavsiye edilir. Göğüs kafesinin esnekliğinden faydalanmak için tercihen yenidoğan döneminde erken cerrahi düzeltme önerilir. Bu yazıda, posterior periosteal flep, sliding kondroplasti ve kıkırdak greft interpozisyonu teknikleriyle başarılı bir şekilde düzeltilmiş, V şeklinde sternal klefti olan iki aylık bir kız hasta sunuldu.

Surgical repair of a sternal cleft malformation

Sternal cleft is a unique congenital chest wall malformation thatresults from failure of sternal fusion early in the embryologicaldevelopment. Surgical correction is advised both to protectmediastinal structures and to restore respiratory dynamics.Early surgical correction, preferably in the neonatal period,is r ecommended i n o rder t o b enefit f rom t he e lasticity o f t hethoracic cage. In this article, we present a two-month-oldfemale patient with a superior V-shaped sternal cleft, which wassuccessfully corrected with posterior periosteal flap, slidingchondroplasty and cartilage graft interposition techniques.

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