Mehtap ÇAVUŞOĞLU, Semra DURAN, Eda ELVERİCİ, Enis YÜKSEL

Dyke-Davidoff-Masson sendromu: olgu sunumu

Dyke-Davidoff-Masson dirençli konvülziyon, serebral hemiatrofi, fasial asimetri, hemipleji veya hemiparezi, mental retardasyon, genişleme ve havalanma artışı, tek taraflı kafatası sendromdur. İlk kez 1933 yılında Dyke ve arkadaşları tarafından tanımlanan bu sendrom, konjenital ve kazanılmış birçok nedene bağlı olarak bildirisinde, DDMS tanısı almış ve epilepsi nedeniyle takip edilen, 36 yaşında mental retarde kadın hastanın tanısal kranial magnetik rezonans görüntüleme bulgularını sunmayı amaçladık.

Dyke-Davidoff-Masson syndrome: a case report

Dyke-Davidoff-Masson syndrome is characterized with drug resistant epileptic seizures, cerebral hemiatrophy, facial asymmetry, contralateral hemiplegia or hemiparesis, mental retardation, unilateral thickening of the skull, extensive widening of paranasal sinuses and increase in air levels. The syndrome was first described in 1933 by Dyke et al. and both congenital and acquired factors are involved in the etiology. In this case report, we aimed to present the diagnostic magnetic resonance imaging findings of a 36-year-old mentally retarded female patient with DykeDavidoff-Masson syndrome.

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