BERNA AKSOY, MAHİ BALCI, Hüseyin ÜSTÜN, Sedef ŞAHİN

Frontal fibrozan alopesi

Amaç: Frontal fibrozan alopesi (FFA) genelde postmenopozal kadınlarda görülen, frontal saç çizgisinde gerilemeye neden olan skatrisyel alopesi ile seyreden bir hastalıktır. Olgu sunumu: Altmış yaşında bayan hasta iki yıldır saç dökülmesi ve alın açılması şikayetiyle başvurdu. Dermatolojik muayenede frontal saç çizgisinde gerileme ve bu alandaki deride atrofi gözlendi. Saçlı deri frontal bölge saç çizgisinden alınan “punch” biyopsinin histopatolojik incelemesinde kıl folliküllerinde sayıca azalma ve büyüklük farkı, perifolliküler fibrozis, perifolliküler hafif lenfoplazmositer infiltrasyon saptandı. Ayrıca subkutan yağ dokusunda üst dermise doğru çekilme gözlendi. Olgunun histopatolojisi liken pilanopilaris olarak rapor edildi. Ancak olgunun kliniğinin çok tipik olması ve histopatolojisinin destekler nitelikte olması nedeniyle olguya frontal fibrozan alopesi tanısı konuldu. Sonuç: Bu olgu vesilesi ile yeni tanımlanan bir klinik antite olan FFA ile ilgili genel bilgi verilmesi amaçlanmıştır.

Frontal fibrosing alopecia

Objective: Frontal fibrosing alopecia (FFA) is a type of cicatricial alopecia characterized by frontal hair line recession. It is usually seen in postmenopausal women. Case report: A 60-year-old woman presented with the complaints of hair loss and frontal hairline recession present for two years. On dermatologic examination frontal hairline recession and skin atrophy involving this scalp area were observed. A punch biopsy specimen taken from the frontal hairline revealed decrease in hair follicle count, variation in hair follicle sizes, perifollicular fibrosis and mild lymphoplasmocytic infiltration. In addition an upward displacement of subcutaneous fat tissue towards the upper dermis was observed. The histopathologic diagnosis was interpreted as lichen planopilaris. However, a diagnosis of frontal fibrosing alopecia was considered as the clinical findings were so typical and histopathological findings were supportive. Conclusion: This article highlights the general features of FFA which is a newly described clinical entity by reporting this case.

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