Berrin IŞIK, Sibel ERYILMAZ, Zeynep DİLMEN

Sturge-Weber Sendromlu Olguda Anestezi Yönetimi

Sturge-Weber Sendromu sporadik olarak ortaya çıkan, konjenital gelişen, nörokutanöz bir hastalıktır. Bu hastalıkta leptomeningeal hemanjiom, trigeminal sinir bölgesine dağılmış genellikle tek taraflı Porto şarabı nevus, oküler anomali (glokom) görülür. Hemanjiomların yerleşimi ve büyüklüğü, intraoküler ve intrakaranyal basıncın korunması anestezi uygulamalarında özel dikkat gerektirir. Bu yazıda genel anestezi altında sağ spermatik kord kisti eksizyonu ve sünnet planlanan 4 yaşındaki erkek olguda anestezi yönetimi sunularak literatür bilgileri ışığında tartışılması hedeflenmiştir.

Anesthetic Management of Patient with Sturge-Weber Syndrome

Sturge-Weber Syndrome is a sporadic, congenital, neuro-cutaneous disease. In this disease, leptomeningeal hemangioma, the unilateral Port wine nevus that distributed in the trigeminal nerve region and ocular anomaly (glaucoma) is usually seen. The placement and size of hemangiomas requires special attention in the practice of anesthesia for the protection of intraocular and intracranial pressures. In this article, we aimed to present anesthesia management under general anesthesia in the case of 4-year-old male who planned the right spermatic cord cyst excision plus circumcision and discussion in the light of literature information.

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