Zamri ZUHDİ, Affirul Chairil ARİFFİN, Razman JARMİN, Hairol Azrin OTHMAN, Azlanuddin AZMAN, Firdaus HAYATİ, Nornazirah AZİZAN

Karaciğerin İndiferansiye Embriyonal Sarkoması: Tanının Gizemi

Yirmi yaşında erkek hasta acil laparotomi gerektiren peritonit ile başvurdu. Sağ lobda büyük bir karaciğer apsesine sahip olduğu tespit edildi. Açık drenaj yapıldı, ancak apse takiben sürekli olarak çözümlenemedi. Bilgisayarlı tomografi (BT), solid karaciğer lezyonu ile birlikte yüksek Ca 19-9 gösterdi. Sağ hepatektomi yapıldı ve histoloji, karaciğerin nadir ve agresif bir embriyonal sarkomu ile uyumluydu. Onkolojik rezeksiyona rağmen lokal rekürrens gelişti ve postoperatif 6 ayda ölümle sonuçlandı. Burada, karaciğer apselerinin benzersiz etiyolojisini, karaciğerdeki indiferansiye embriyonal sarkomun literatür bilgilerini tanımladık.

Undifferentiated Embryonal Sarcoma of the Liver: An Enigma of Diagnosis

A 20-year-old man presented with peritonitis requiring emergencylaparotomy. He was found to have a huge liver abscess on the right lobe. Opendrainage was performed but the abscess was persistently unresolved uponfollow up. Computed tomography (CT) revealed a solid liver lesion with raisedCa 19-9. Right hepatectomy was subjected and histology was consistent witha rare and aggressive case of embryonal sarcoma of the liver. Despiteoncologic resection, he developed local recurrence and succumbed to deathin 6 month postoperatively. We describe a unique aetiology of liver abscesswith literature reviews of undifferentiated embryonal sarcoma of the liver.

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