Dış Kulak Yolu Adenoid Kistik Karsinomu
Dış kulak yolunu içeren primer malignite nadirdir, bunların % 80'inde skuamöz hücreli karsinom,% 5'inde adenoid kistik karsinom vardır. Bu tümörler yüksek nüks oranları, cerrahi tedavi ve adjuvan radyoterapiden kaynaklanan önemli morbiditeler ve ayrıca hastanın ölümüyle bilinirler. Yineleyen sağ kulak ağrısı ile başvuran sağ kulak kanal kitlesi olan yaşlı bir kadın olgusunu sunuyoruz. Tümör eksize edildikten sonra adenoid kistik karsinom olduğu doğrulandı. Bu vaka, dış kulak yolunu içeren adenoid kistik karsinomların varlığının nadir olduğunu göstermektedir ve gizli başlangıcı klinik olarak iyi huylu bir durum olarak yanlış anlaşılabilir.
External Ear Canal Adenoid Cystic Carcinoma
Primary malignancy involving the external auditory canal is rare, with 80% ofthem being squamous cell carcinoma while 5% of them are adenoid cysticcarcinoma. These tumours are known for its high rates of recurrence,significant morbidities from surgical management and adjuvant radiotherapy,as well as eventual death of the patient. We describe a case of an elderlyfemale with right ear canal mass who presented with recurrent right ear pain.After the tumour was excised, it was confirmed to be adenoid cysticcarcinoma. This case highlights the rarity of the entity of adenoid cysticcarcinomas involving the external auditory canal; and how its subtle initialpresentation can be mistaken to be a clinically benign condition.
___
- Kokemueller H, Eckardt A, Brachvogel P et al. Adenoid cystic carcinoma of
the head and neck—a 20 years experience. International Journal of Oral and
Maxillofacial Surgery. 2004;33:25-31.
- Berdal P, Besche Ad, Mylius E. Cylindroma of salivary glands a report of 80
cases. Acta Oto-Laryngologica. 1970;69:170-3.
- Szanto PA, Luna MA, Tortoledo ME et al. Histologic grading of adenoid cystic
carcinoma of the salivary glands. Cancer. 1984;54:1062-9.
- Zainor S, Mamat H, Saad SM et al. Adenoid cystic carcinoma of external
auditory canal: A case report. Egyptian Journal of Ear, Nose, Throat and Allied
Sciences. 2013;14:41-4.
- Spiro RH. Salivary neoplasms: Overview of a 35-year experience with 2,807
patients. Head & Neck. 1986;8:177-84.
- Perzin KH, Gullane P, Conley J. Adenoid cystic carcinoma involving the
external auditory canal a clinicopathologic study of 16 cases. Cancer.
1982;50:2873-83.
- Dong F, Gidley PW, Ho T et al. Adenoid cystic carcinoma of the external
auditory canal. The Laryngoscope. 2008;118:1591-6.
- Waldron CA, El-Mofty SK, Gnepp DR. Tumors of the intraoral minor salivary
glands: a demographic and histologic study of 426 cases. Oral Surgery, Oral
Medicine, Oral Pathology. 1988;66:323-33.
- Bhatt MC. A rare case of adenoid cystic carcinoma of ceruminous gland of
EAC. Otolaryngology Online Journal.2016;6:101.
- Silverman DA, Carlson TP, Khuntia D et al. Role for postoperative radiation
therapy in adenoid cystic carcinoma of the head and neck. The Laryngoscope.
2004;114:1194-9.