Meltem AKÇABOY, Saliha ŞENEL, Mehpare ÖZKAN, Serkan ÇİFTÇİ, Eyüp SARI, Hüsniye YÜCEL

İnfant Dönemde Akut Dissemine Ensefalomyelit (ADEM) Tanısı ile İzlenen İki Hasta: Olgu Sunumu

Akut dissemine ensefalomyelit, çeşitli nörolojik belirtiler ile görülenmonofazik, inflamatuar, demyelinizan bir santral sinir sistemi hastalığıdır.Çocukluk yaş grubunda infant dönemde görülmesi nadirdir. Burada 2 yaşınaltında akut nörolojik belirtiler ile başvuran ve ileri değerlendirme sonucundaakut dissemine ensefalomyelit tanısı konulan, iki hasta sunulmaktadır. Akutdissemine ensefalomyelit tanısı klinik ve nörogörüntüleme ile konulmaktadır.Spesifik olmayan enfeksiyon belirtileri ya da aşılama sonrasında ortaya çıkanakut nörolojik semptomlar ve ensefelopati varlığında ayırıcı tanı da akutdissemine ensefalomyelit akla gelmelidir. Tedavide yüksek dozkortikosteroidler ilk seçenek olarak kullanılmaktadır.

Acute Disseminated Encephalomyelitis (ADEM) is Available in Infancy: Case Reports of Two Patients

Acute disseminated encephalomyelitis is a monophasic, inflammatory, demyelinating central nervous system disease with various neurological manifestations. The diagnosis of the disease during infancy is rare in childhood age group. Here we present two patients who are under 2 years-old and presented with acute neurological symptoms and diagnosed as acute disseminated encephalomyelitis the result of further evaluation. Acute disseminated encephalomyelitis is diagnosed upon clinical and neuroimaging findings. Acute disseminated encephalomyelitis should be considered in the differential diagnosis of acute neurological symptoms or encephalopathy occurring after vaccination and non-specific infections. High dose corticosteroids are used successfully in the treatment.

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