Onur IŞIK, Tolga BAŞ, Murat KOÇ, Hakan AYDIN, Ali KUTSAL

Parsiyel anormal pulmoner venöz dönüş anomalisi ile intakt atrial septum birlikteliği: Nadir bir konjenital anomali

ntakt atriyal septumlu parsiyel anormal pulmoner venöz dönüş anomalisi çocuk yaş grubunda genellikle asemptomatiktir. Çoğu zaman elimizdeki rutin tanı araçları olan EKG, telekardiyografi, ekokardiyografi hatta kateter anjiyografi ile tanınması zordur. Kliniğimizde tanı alan ve cerrahi olarak tedavi edilen hastamızı anomalinin karakteristikleri, klinik gidiş, tanı araçları ve cerrahi tedavi statejileri yönlerinden tartıştık

Partial anomalous pulmonary venous return with intact atrial septum: A rare congenital anomaly

Partial anomalous pulmonary venous return with intact atrial septum anomaly is usually asymtomatic in pediatric population. Diagnose of this anomaly can be challenging with our routine eveluation methods like ECG, telecardiography, echocardiography and even catheter angiography. We discussed the anomalous characteristics, clinical progression, and diagnostic methods and surgical strategies employed for a patient diagnosed and undergoing surgical treatment in our clinico.

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