Kerem ERKALP, Zehra YANGIN, Şule KIROĞLU

Noonan sendromunda anestezi uygulaması (Olgu sunumu)

Noonan sendromu, kardiyovasküler, iskelet, hematolojik ve santral sinir sistemi anomalileri ile yüz anomalilerinin birlikte görüldüğü nadir klinik bir durumdur. Sendromun nadir olmasına bağlı olarak, literatürde az sayıda hastada anestezi uygulanmıştır. Noonan sendromunda görülebilen birçok anomaliler anestezisi için zorluk oluşturabilir. Bu olgu sunumunda, vulvar hemanjiom eksizyonu nedeniyle ameliyata alman, Noonan sendromlu 21 yaşındaki kadın hastaya uyguladığımız anestezi yöntemini tartışmayı ve bu sendromun anestezi uygulaması açısından önemli olan özelliklerini vurgulamayı amaçladık.

Anahtar Kelimeler:

Hemanjiyom, Noonan sendromu, Larinks maskeleri

Anesthetic management of a patient with Noonan's syndrome (Case report)

Noonan's Syndrome is a rare clinical condition associated with cardiovascular, skeletal, facial, hematological and central nervous systems abnormalities. Owing to the rarity of the syndrome, few cases of anesthesia use for this syndrome have been described in the literature. The wide variety of abnormalities which may be encountered in Noonan's syndrome present a dilemma for the anesthetist. A 21-year-old girl with Noonan's syndrome underwent vulvar hemangioma excision. In this case study, our aim was to describe the anesthetic management of the patient and the potential multiple problems resulting from the facial, cardiovascular, skeletal and airway abnormalites associated with this condition.

Keywords:

Hemangioma, Noonan Syndrome, Laryngeal Masks,

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