Necmettin ÇOLAK, Yunus NAZLI, İnci Aslı ATAR, Reyhan BAYRAK, Ömer Nuri AKSOY, İsmail Olgun AKKAYA, Ömer ÇAKIR

Left Atrial Myxoma of Atypical Origin and Pulmonary Sarcoidosis: An Uncommon Association

Sarkoidoz histolojik olarak pek çok dokuda granulom oluşumu ile karakterize multisystem hastalığıdır. Pulmoner tutulum sık olamasına rağmen kardiyak sarkoidoz nadirdir. Miksomalar benign kardiyak tümörlerin en yaygın tipidir ve genellikle sol atriyum içinde fossa ovalis etrafındaki sol atriyal septuma yapışıktır. Biz burada pulmoner sarkoidozlu bir hastada atipik orijinli dev sol atriyal miksomanın başarılı olarak cerrahi eksizyonunu tanımladık. Miksoma sol atriyumun posteromedial duvarına bağlıydı. Hastamızda pulmoner sarkoidoz mevcuttu, fakat aile hikayesinde sarkoidoz ya da kardiyak miksoma yoktu.

(Atipik orijinli sol atriyal miksoma ve pulmoner sarkoidoz: nadir birliktelik)

Sarcoidosis is a multisystem disease characterrized histologically by the formation of granulomas in many tissues. Although pulmonary involvement is frequent, cardiac sarcoidosis is rare. Myxomas are the most common type of benign cardiac tumor and are usually located in the left atrium and are attached to the left atrial septum around the fossa ovalis. We describe herein the successful surgical removal of a moderate diameters left atrial myxoma of atypical origin in a patient with pulmonary sarcoido-sis. It was attached to the posteromedial wall of the left atrium. Our patient had pulmonary sarcoidosis, but had no family history of sarcoidosis or cardiac myxoma.

PDF

___

1. Dubrey SW, Falk RH. Diagnosis and management of cardiac sarcoidosis. Prog Cardiovasc Dis 2010;52:336-46.
2. Shapiro LM: Cardiac tumours: diagnosis and management. Heart 2001;85:218-22.
3. Cetinkaya E, YÕlmaz A, Özgül A, Genço÷lu A, Günlüo÷lu G. Left atrial mass demonstrated during endobronchial ultrasound session. Respiration 2011;81:57-8.
4. Carney JA, Gordon H, Carpenter PC, et al. The complex of myxomas, spotty pigmentation, and endocrine overactivity. Medicine (Baltimore) 1985;64:270-83.
5. Habersberger J, Manins V, Taylor AJ. Cardiac sarcoidosis. Intern Med J 2008;38:270-77.
6. Butany J, Bahl NE, Morales K, et al. The intricacies of cardiac sarcoidosis: a case report involving the coronary arteries and a review of the literature. Cardiovasc Pathol 2006;15:222-27.