RECEP BEDİR, Remzi Adnan AKDOĞAN, İbrahim ŞEHİTOĞLU

Primary Signet Ring Cell Carcinoma of the Appendix: A Rare Case Report

Apendikste primer taşlı yüzük hücreli karsinom oldukça nadir görülmekte olup, tüm appendiks tümörlerinin %0,5den azını oluşturur. Sunduğumuz olguda akut apendisit ön tanısı nedeniyle operasyona alınan ve apendikste kitle görülmesi üzerine sağ hemikolektomi yapılan hastanın, sağ hemikolektomi materyalinin patolojik incelemesinde apendiksi diffüz tutan kas tabakaları arasında infiltrasyon gösteren iri hiperkromatik nükleuslu taşlı yüzük görünümünde atipik epitelyal hücrelerden oluşan taşlı yüzük hücreli karsinom izlenmiştir. Olgumuzun appendikste oldukça ender görülmesi ve prognozunun appendiksin klasik adenokarsinomlarından kötü olması nedeni ile sunulmaya değer bulunmuştur.

(Appendiksin Primer Taşlı Yüzük Hücreli Karsinomu: Olgu Sunumu)

Primary signet ring cell carcinoma is rarely seen in appendix and accounts for less than 0.5% of all tumors of the appendix. In our case due to the diagnosis of acute appendicitis, patient was operated and right hemicolectomy was performed when a mass in the apendix was observed. Pathology of right hemicolectomy revealed signet ring cell carcinoma that large hyperchromatic nuclei with signet ring appearance of atypical epithelial cells which diffusely infiltrated muscle layers. We presented the case because its occurence in apendix is very rare and prognosis is poorer than the classical adenocarcinomas of apendix.

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