Buğra HARMANDAR, Filiz COŞKUN, Ahmet ŞAŞMAZEL, İlker Kemal YÜCEL, Ahmet BOLUKÇU, Ahmet ÇELEBİ, Numan Ali AYDEMİR, Ali Rıza KARACI

Surgical treatment of double aortic arch

Amaç: Bu çalışmada, izole çift arkus aort (ÇAA) olgularında tedavi yaklaşımı ve cerrahi sonrası sonuçları tanımlandı.Çalışmaplanı:Ocak 2006 - Ocak 2012 tarihleri arasında ÇAA nedeniyle ameliyat edilen 11 hastanın (8 kız, 3 erkek; ort. yaş 18.6 ay) başvuru bilgileri, tedavileri ve ameliyat sonuçları ile ilgili veriler retrospektif olarak değerlendirildi. Semptomların düzelme süresi takip dönemi boyunca kaydedildi.Bul gu lar: Semptomların başlangıcında ortalama yaş 3.5 aydı (doğumdan 4 yaşa kadar). Gastrointestinal semptomlar tüm hastalarda mevcutken respiratuar semptomlar hastaların %45.5'inde bulunmaktaydı ve en sık görülen semptomlar sırasıyla beslenme güçlüğü ve tekrarlayan solunum yolu enfeksiyonlarıydı. Tüm hastalara düzeltici cerrahi başarıyla uygulandı. Erken veya geç ölüm meydana gelmedi. Takiplerde yeniden cerrahi ihtiyacı olmadı. Gastrointestinal sistemi içeren semptomlar tüm hastalarda (%100) ortalama 6.4±4.3 ayda düzelirken respiratuar semptomlar dört hastada (%80) ortalama 11.4±7.2 ayda düzeldi.So nuç: Günümüzde, ÇAA'nın cerrahi tedavisinin sonuçları tatmin edicidir. Cerrahi sonrasında, yaştan bağımsız olarak tüm hastalarda gastrointestinal semptomlar kaybolurken respiratuar semptomların tam düzelmesi için erken girişim yapılması gerekmektedir.

Çift arkus aortun cerrahi tedavisi

Background: This study aims to describe the management and surgical outcomes of patients with isolated double aortic arch (DAA). Methods: Data regarding presentation, management, and surgical outcomes of 11 patients (8 girls, 3 boys; median age of 18.6 months) operated between January 2006 and January 2012 due to DAA were evaluated retrospectively. Duration of the reversal of symptoms was recorded throughout the follow-up period. Results: The median age at the onset of symptoms was 3.5 months (birth to 4 years). Gastrointestinal symptoms were present in all and respiratory symptoms were present in 45.5% of patients, with difficulty in feeding and recurrent respiratory tract infections being the most common symptoms, respectively. All patients underwent corrective surgery successfully. No early or late death occurred. No reoperations were required during follow-ups. Symptoms involving gastrointestinal tract disappeared in all patients (100%) in mean 6.4±4.3 months, whereas respiratory symptoms disappeared in four patients (80%) in 11.4±7.2 months. Conclusion: Today, results of surgical treatment of DAA are satisfying. Following surgery, while gastrointestinal symptoms disappeared in all patients regardless of age, complete relief of respiratory symptoms requires early intervention.

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