Hülya SUNGURTEKİN, Ali Vefa ÖZCAN, Ahmet BALTALARLI, Gökhan ÖNEM, İbrahim GÖKŞİN, Mustafa SAÇAR

"Right atrial-jugular vein graft bypass" for treatment of superior vena cava syndrome caused by protein S deficiency

Otuz iki yaşında kadın olguya protein S eksikliğine bağlı olarak gelişmiş vena kava süperiyor sendromu tanısı konuldu. Üç aylık tıbbi tedavi sürecinde hastanın semptomlarında gerileme sağlanamadı. Sağ atriyo-jugüler ven greft bypass uygulanan hastanın yakınmaları 10 günde geriledi. Ameliyat sonrası 18 aylık takip süresince herhangi bir komplikasyon gelişmedi. Olgu ilgili literatür eşliğinde sunuldu.

Protein S yetmezliğine bağlı gelişen vena kava süperiyor sendromunun tedavisi için "sağ atriyo-jugüler ven greft bypass"

Superior vena cava syndrome from protein S deficiency was diagnosed in a 32 year-old female. A three month period of medical treatment did not relieve her symptoms. We performed a “right atrial-jugular vein graft bypass” which relieved her symptoms within 10 days. The patient did not develop any complications in the 18 month postoperative period. We present this case with a review of the relevant literature.

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