İlker ERTUĞRUL, Utku Arman ORUN, Murat KOÇ, Tamer YOLDAŞ, Selmin KARADEMİR, Vehbi DOĞAN, Senem ÖZGÜR

iventriküler dolaşımlı kritik aort darlığı ile ilişkili endokardiyal fibroelastozisli hastaların klinik özellikleri ve sonuçları

Amaç: Bu çalışmada kritik aort darlığına bağlı endokardiyal fibroelastozisi olan hastaların özellikleri, bulguları ve prognozu değerlendirildi.Çalışma planı: Çalışmaya Ocak 2008 - Temmuz 2014 tarihleri arasında kritik aort darlığına eşlik eden endokardiyal fibroelastozisi olan 22 yenidoğan (17 erkek, 5 kız; ort. yaş 7.5 gün; dağılım 0-28 gün) dahil edildi. Hastaların demografik, ekokardiyografik ve kardiyak kateterizasyon ve anjiyografi bulguları incelendi.Bul gu lar: Hastaların başvuru anındaki ortalama vücut ağırlıkları 3.3 kg (dağılım 2-4.8 kg) idi. Hastaların %90'ında değişik derecelerde sol ventrikül sistolik disfonksiyonu (ejeksiyon fraksiyonu

Clinical characteristics and outcomes in patients with endocardial fibroelastosis associated with critical aortic stenosis with biventricular circulation

Background: This study aims to assess the characteristics, results and prognosis of patients with endocardial fibroelastosis secondary to critical aortic stenosis.Methods: The study included 22 newborns (17 boys, 5 girls; mean age 7.5 days; range 0 to 28 days) having endocardial fibroelastosis associated with critical aortic stenosis between January 2008 and July 2014. Patients' demographic, echocardiographic and cardiac catheterization, and angiography findings were reviewed.Results: Patients' mean weight at presentation was 3.3 kg (range 2 to 4.8 kg). Left ventricular systolic dysfunction with varying degrees (ejection fraction

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