Ertürk KARAAĞAÇ, Nihan YEŞİLKAYA, Tahsin Murat TELLİOĞLU, Fulya ÇAKALAĞAOĞLU ÜNAY, Yüksel BEŞİR

A rare cardiac tumor presenting with myxoma: Primary cardiac hemangioendothelioma

Epithelioid hemangioendothelioma is a rare malignant vascular tumor which originates from the vascular endothelial or dendritic cells and has a moderate malignancy between benign hemangioma and malignant hemangiosarcoma, arising from vascular structures. Radical resection of epithelioid hemangioendothelioma is recommended, due to both its malignant nature and the adverse effects of associated complications on mortality and morbidity. In this article, we present a rare case of primary cardiac epithelioid hemangioendothelioma accompanied by a left atrial myxoma which was treated by resection.

Miksomaya eşlik eden nadir bir kalp tümörü: Primer kardiyak hemanjioendotelyoma

Epiteloid hemanjioendotelyoma, vasküler endotelyal veya dentritik hücrelerden köken alan, benign hemanjiyom ile malign hemanjiyosarkom arasında orta derecede maligniteye sahip, vasküler yapılardan kaynaklanan nadir görülen malign bir vasküler tümördür. Epiteloid hemanjioendotelyomanın radikal rezeksiyonu, hem tümörün malign yapısı, hem de ilişkili komplikasyonlarının mortalite ve morbidite üzerine olumsuz etkileri nedeniyle önerilmektedir. Bu yazıda, rezeksiyon ile tedavi edilen sol atriyal miksomanın eşlik ettiği nadir bir primer kardiyak epiteloid hemanjioendotelyoma olgusu sunuldu.

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