Alkım YOLCU, Cumhur Murat TULAY, Peyker TEMİZ, İsmet AYDOĞDU

Langerhans cell histiocytosis: A rare cause of pathological rib fracture

Langerhans cell histiocytosis, formerly known as histiocytosis X, represents clonal proliferations of the antigen-presenting dendritic cells, which are normally found in many organs. It is a rare disease which tends to affect children and adolescents. In particular, adult-onset type is very rare. Herein, we present a female adult diagnosed with Langerhans cell histiocytosis of the rib without any systemic involvement which was successfully treated with surgery.

Langerhans hücreli histiyositoz: Patolojik kaburga kırığının nadir bir nedeni

Daha önceleri histiyositoz X olarak da bilinen Langerhans hücreli histiyositoz, normalde birçok organda bulunan antijen sunan dendritik hücrelerin klonal proliferasyonlarını temsil eder. Bu, çocukları ve ergenleri etkileme eğiliminde olan nadir bir hastalıktır. Özellikle, erişkin başlangıçlı formu çok nadirdir. Bu yazıda, herhangi bir sistemik tutulumu olmayan, kostal Langerhans hücreli histiyositoz tanısı konan ve cerrahi ile başarılı bir şekilde tedavi edilen erişkin bir kadın olgu sunuldu.

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