Emine AZAK, İbrahim İlker ÇETİN, TEVFİK KARAGÖZ, Metin DEMİRCİN

rare association of left pulmonary artery sling with Scimitar syndrome: Recurrent wheezing and respiratory distress in a pediatric patient

Congenital anomalies of the heart and great vessels may lead to localized recurrent pulmonary infections through different mechanisms. Pulmonary artery sling (left pulmonary artery originating from the right pulmonary artery) and Scimitar syndrome are rare causes of wheezing in infants. An 18-month-old female infant with left pulmonary artery sling, Scimitar syndrome, and an anomalous connection of left pulmonary veins to the left atrium was admitted to our clinic. She successfully underwent transcatheter embolization using the Vascular Plug-II on the anomalous systemic arterial supply and repair of pulmonary arterial sling and Scimitar anomaly via a median sternotomy. In conclusion, diagnosis of left pulmonary arterial sling accompanied by abnormalities can be missed in some cases using echocardiography. It may be necessary to conduct more advanced imaging methods before deciding the treatment method to be performed in these patients.

Sol pulmoner arter sling ve Scimitar sendromunun nadir birlikteliği: Bir çocuk hastada tekrarlayan hırıltı ve solunum sıkıntısı

Kalbin ve büyük damarların doğumsal anomalileri, farklı mekanizmalar ile tekrarlayan lokalize pulmoner enfeksiyonlara yol açabilir. Pulmonar arter sling (sol pulmoner arterin sağdan köken alması) ve Scimitar sendromu, bebeklerde hırıltılı solunumun nadir nedenlerindendir. Sol pulmoner arter sling, Scimitar sendromu ve sol pulmoner venlerin sol atriyuma anormal bağlantısı olan 18 aylık bir kız bebek kliniğimize başvurdu. Başarılı bir şekilde Vasküler Plug-II ile anormal sistemik arter kaynağı transkateter yolla embolize edilerek, medyan sternotomi yoluyla pulmoner arter sling ve Scimitar anomalisi düzeltildi. Sonuç olarak, ekokardiyografi ile bazı olgularda anormalliklerin eşlik ettiği pulmoner arter sling tanısı gözden kaçırılabilir. Bu hastalarda yapılacak tedavi yöntemine karar vermeden önce, daha ileri görüntüleme yöntemlerinin uygulanması gerekebilir.

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