Yetkin AĞAÇKIRAN, Ahmet KUŞDEMİR, Ayşegül AKSOY ALTINBOĞA, Merve Meryem KIRAN

Nadir Görülen Bir Lezyon; Dalağın Sklerozan Anjiomatoid Nodüler Transformasyonu; Olgu Sunumu

Sklerozan anjiomatoid nodüler transformasyon (SANT); dalağın nadir görülen benign vasküler bir lezyonudur. Görüntüleme tekniklerinin gelişmesi ve kullanımının artması nedeniyle genellikle insidental olarak saptanmaktadır. İlk olarak Martel ve arkadaşları tarafından 2004 yılında 25 vakalık bir serinin incelenmesi sonucunda tanımlanmıştır. Makroskopik olarak dalakta, ortasında skar alanı bulunan sarı kahverengi solid nodül gözlenir. Histolojik olarak sklerotik stroma ile çevrili multiple nodüller ile karakterizedir. Nodüller vasküler yapılardan oluşmaktadır. Bu vasküler yapıların duvarı şişkin endotel hücreleri ile döşelidir. Atipi, mitoz ya da nekroz görülmez. Gelişimi Ebstein- Barr virüs, dolaşım bozuklukları gibi nedenler ile ilişkilendirilmekle birlikte etiyolojisi net değildir.Dalakta kitle nedeniyle splenektomi geçiren, 37 yaşında erkek hastaya ait bir olgu burada sunulacaktır

A Rare Lesion; Sclerosing Angiomatoid Nodular Transformation Of Spleen; Case Report

Sclerosing angiomatoid nodular transformation (SANT); is a rare benign vascular lesion of the spleen. SANT is usually detected insidentally with improvement and increasing use of radiologic techniques. It was first described in 2004 by examining 25 case by Martel et al.Macroscopically there is a yellow-brownish solid nodul with santral scar in the spleen. Histolopathologically it is characterised by multiple nodules which is surrounded by a sclerotic stroma. Each nodule is composed of vascular structures. Vascular structures are lined by plump endothelial cells. Nuclear atypia, necrosis and mitoses are absent. Pathogenesis of this lesion is not clear. Although there is some literature that claimed it is association with Ebstein- Barr virus and some circulatory collapse.Herein this paper, we report 37 years old male patient who undergone splenectomy for a splenic mass

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