SWYER-JAMES (MACLEOD) SENDROMU:BİR OLGU SUNUMU
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Swyer-James (MacLeod) Syndrome: A Case Report
Swyer-James syndrome is a radiologic entity characterized by hyperlucency of one or several lobes, or even of one lung, scarce hilar shadow on the same side as the transradiency, and barely visible arterial network on the abnormal side of the thorax. Generally, it is acquired subsequent to viral bronchopulmonary infections in child-hood. A seven year old boy was admitted to our hospital with complaining of a cough. He had been hospitalised for bronchopulmonary infections when he was one year old. During follow up, hyperlucency of the left lung was seen on his chest x-ray. However, sweat testing and bronchoscopy examinations were found normal. Physical examination showed markedly decreased breathing sounds in the left hemitorax with fine inspiratory crackles and expiratory wheezes. The chest x-ray revealed hyperlucency of the left lung. A diagnosis of Swyer James syndrome was confirmed by computerized tomographic scans of chest and perfusion and ventilation lung scintigraphy. Computerized tomography findings were hyperlucency and decreased volume of left lung and thin pulmonary artery branches. Small left lung parenchyma and decreased perfusion were found on radionuclide scans. The scan showed markedly diminished ventilation, diminished vascular flow and diminished perfusion unilaterally on the left lung. We suggest that this condition should be considered during the differential diagnosis of a patient with unilaterally hyperlucent lung.
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- 1. Orenstein DM. Emphysema and Overinflation. In:
Behrman RE, Kliegman RM, Arvin AM (eds). Nelson
Textbook of Pediartics. Philadelphia, London, Toronto,
Montreal, Sydney, Tokyo. W.B. Saunders Company
1996: 1227-8.
- 2. Mayeux I, Aubry P, Jouniesux V. Syndrome de SwyerJames ou Macleod ou poumon clair unilateyeral. Presse
Med 1996; 25: 929-32
- 3. King ET. Bronchiolitis. In:Fishman AP, Elias JA, Fishman
JA, Grippe MA (eds). Pulmonary Diseases and Disorders. St Luis . McGraw-Hill Com.1998; 825-63.
- 4. Lucaya J, Gartner S, Garcia-Pena P, Cobos N, Roca I,
Linan S. Spectrum of manifestations of Swyer-JamesMacLeod syndrome. J Comput Assist Tomogr 1998;
22: 592-7.
- 5. Hekali P, Halttunen P, Korhola O, Korppi-Tommola T.
Chronic unilateral hyperlucent lung. A consecutive series of 40 patients. ROFO Fortschr Geb Rontgenstr
Nuklear Med 1982; 136: 41-8
- 6. Chevrolet JC, Junod AF. A characterics of respirtory
functional involvement in MacLeods syndrome (or
Swyer-James syndrome). Schweiz Med Wochenschr
1987; 117: 1902-9.
- 7. Avital A, Shulman DL, Bar-Yishay E, Noviski N,
Schachter J, Krausz Y, Godfrey S. Differential Lung function in an ýnfant with the Sweyer-James syndrome. Torax
1998; 44: 298-302.
- 8. Wong KS, Chen HW, Yan DC, Lin TY. Swyer James
syndrome following mycolpasma pneumonia. Chung
Hua Min Kuo Hsiao Erh Ko I Hsueh Hui Tsa Chih
1998; 39: 271-3.