Nafiz SARIŞIK, Can ACIPAYAM, Ahmet Gökhan GÜLER, Abdülkadir Yasir BAHAR, Betül KIZILDAĞ, Fatih TEMİZ

Small İntestine İntussusception Accompanying With Bilateral Adrenal Mass In A 11 Years Old Child With Burkitt Lymphoma

The Gastrointestinal system is one of the most common places for extranodal Non-Hodgkin lymphomas. On the other hand, Non-Hodgkin lymphomas have been seen less in the small intestine. We present here a rare condition in the literature which is a case of bilateral adrenal mass and Burkitt lymphoma with small intestine origin. Eleven years old male patient applied to pediatric emergency service with acute abdomen. In the abdominal USG examination intussusception and bilateral adrenal mass had seen. In a surgical operation, five lesions were seen in the small intestine. Partial small intestine resection was performed. In the pathological examination of the resection material Burkitt Lymphoma with the origin of the small intestine diagnosed to the patient. Prognosis of NHL with the origin of the small intestine, adrenal mass and come with an acute abdomen depends on the histological type and grade. He was started on NHL-BFM95 chemotherapy and had a good clinical response and he was remained in complete remission for two months after completion of chemotherapy. Bilateral adrenal mass remains a rare form of Burkitt lymphoma and care must be taken in ruling out other causes of bilateral adrenal masses.

Anahtar Kelimeler:

Primary adrenal mass, Non-Hodgkin lymphoma, small intestine

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