Ali YİLDİRİM, Savaş DEMİRPENÇE, Bülent KOCA, Hasan Tolga ÇELİK, Sena ÜNVERDİ

Yenidoğanda Ciddi Kalp Yetersizliğinin Nadir Bir Nedeni: Galen Ven Malformasyonu

Galen ven anevrizmal malformasyonu 1/25000 canlı doğumda görülen, yenidoğan döneminde ciddi mortalite ve morbidite ile seyreden, intrakraniyal anevrizmadır. Yenidoğanda genellikle yüksek debili kalp yetersizliği ve pulmoner hipertansiyon bulgularıyla karşımıza çıkmaktadır. Postnatal ilk gününde solunum sıkıntısı ve siyanoz nedeniyle yoğun bakım ünitesine yatırılan erkek bebekte pulmoner hipertansiyon tespit edilmiş. Magnezyum sulfat ve fosfodiesteraz inhibitörü başlanan hastada multiorgan yetersizliği gelişmesi nedeniyle tarafımıza yönlendirildi. Pulmoner hipertansiyon tespit edilen hastanın inen aortasında diyastolik ters akım saptanması nedeniyle yapılan kraniyal ultrasonografide galen ven anevrizması tespit edildi. İlerleyici kalp yetersizliği ve pulmoner hipertansiyon ile başvuran postnatal 20 günlük erkek bebekte tespit edilen galen ven anevrizma vakasını sunduk.

Anahtar Kelimeler:

Yenidoğan, kalp yetersizliği, Galen Ven Malformasyonu

Neonate With Severe Heart Failure Related To Vein Of Galen Malformation

Vein of Galen aneurysmal malformation is a type of intracranial anerysm occurring in 1/25000 live-births that is characterized by significant morbidity and mortality during the newborn period. Newborns with this condition generally present with high-output cardiac failure and pulmonary hypertension. A male infant admitted to the intensive care unit on postnatal day 1 due to respiratory distress and cyanosis was found to have pulmonary hypertension. Treatment with magnesium sulfate and phosphodiesterase inhibitor was administered. However, due to the development of multiorgan failure, the patient was referred to our unit. Pulmonary hypertension was confirmed and diastolic reverse flow was detected in the descending aorta. A subsequent cranial ultrasound examination showed the presence of Galen vein aneurysm. Herein, a 20-day old male patient presenting with progressive cardiac failure as well as pulmonary hypertension who was diagnosed to have Galen vein aneurysm is described

Keywords:

Neonate, heart failure, malformation of Galen Vein,

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