Hamide MELEK, Reşit KÖKEN, Ayşegül BÜKÜLMEZ, Tolga Altuğ ŞEN, Tevfik DEMİR, Elvan BAHÇELİ

Melkersson-Rosenthal Sendromu: Bir Olgu Sunumu

Melkersson Rosenthal sendromu tekrarlayan periferik fasiyal paralizi, orofasiyal ödem ve fissürlü dil triadı ile karakterize nöro-mukokütan granülomatöz bir hastalıktır. Çocukluk çağında nadir görülen bu sendrom hayatın 2. ve 3.dekadında daha sık görülür. Klasik triadın görülmesi nadirdir ve genellikle monosemptomatik veya oligo semtomatiktutulum izlenir. Bulgulardan bir veya ikisi ile biyopside granülamotöz keilitin varlığı tanı için yeterlidir. MelkerssonRosenthal sendromu tekrarlayan fasiyal paralizilerin ayırıcı tanısında düﬂünülmesi gereken bir hastalıktır. Bu yazıdaMelkersson Rosenthal sendromu tanısı alan 9 yaşında erkek hasta sunulmuştur.

Anahtar Kelimeler:

Melkersson Rosenthal sendromu, tekrarlayan fasiyal paralizi, orofasiyal ödem, dilde fissür

Melkersson-Rosenthal Syndrome: ACase Report

Melkersson-Rosenthal Syndrome is a neuro-mucocutaneous granulomatous disease. It is characterized by recurrentfacial nerve paralysis, orofacial edema and fissured tongue. This syndrome is very rare in childhood, it is more frequently seen in the second and the third decades of life. Classical triad of this syndrome is very rarely seen. MRS usually occurs as monosymptomatic or oligosymptomatic involment. The presence of two or one of the manifestationswith granulomatous cheilitis in the biopsy is sufficient to make the diagnosis of Melkersson-Rosenthal Syndrome. Indifferential diagnosis of recurrent facial paralysis Melkersson-Rosenthal Syndrome must be considered. We present a9 years old-boy who diagnosed as Melkersson-Rosenthal Syndrome

Keywords:

Melkersson Rosenthal Syndrome, recurrent facial palsy, orofacial edema, fissured tongue,

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