Suraya OTHMAN, Nor Faezan Abdul RASHİD, Shahrun Niza Abdullah SUHAİMİ, Rohaizak MUHAMMAD, Norasyikin A. WAHAB

Kistik lenfanjioma: Adrenal Bezin Nadir Bir Hastalığı

Kistik adrenal neoplaziler seyrektir ve tesadüfen bulunabilir veya semptomatik olabilirler, ancak kistik lenfanjiom nadir görülen benign bir tümördür. Tümör genellikle boyun veya aksillada görülür ve nadiren adrenal bezi tutar. Bu olguda, 3 haftadır anoreksi, kusma ve letarji belirtileri gösteren 42 yaşındaki kadın vakayı sunuyoruz. Hafif dehidratasyon dışında, herhangi bir pozitif fizik muayene bulgusu saptanmadı. Yatış sonrası, kan üre ve kreatinin değerleri yüksekti ve kronik glomerülonefrite sekonder son dönem böbrek hastalığı tanısı aldı. Karın ultrasonunda tesadüfen sağ adrenal kitle ve bilgisayarlı tomografide (CT) ise düz, venöz ve gecikmiş fazda Hounsfield ünitesi (HU) 13, 20 ve 21 olan bir lezyon gösterdi ve % 12.5'lik mutlak yıkanma sağladı. Biyokimyasal testler, fonksiyonel olmayan adrenal insidentaloma ile uyumlu idi. Bu nedenle, adrenal malignite şüphesi nedeniyle sağ retroperitoneoskopik adrenalektomi yapıldı. Bununla birlikte histopatoloji ender görülen adrenal kistik lenfanjiom olarak rapor edilmiştir.

Cystic Lymphangioma: A Rare Disease of the Adrenal Gland

Cystic adrenal neoplasms are uncommon and may be discovered incidentally ormay be symptomatic but cystic lymphangioma is a rare benign tumour. Thetumour usually occurs in the neck or axilla and rarely involves the adrenal gland.Here we report a case of a 42-year-old lady presented with symptoms ofanorexia, vomiting and lethargy for 3 weeks. Apart from evidence of milddehydration, there was no positive physical examination. Upon admission, herblood urea and creatinine was high and she was diagnosed with end stage renaldisease secondary to chronic glomerulonephritis. Ultrasound of the abdomenrevealed an incidental right adrenal mass and computed tomography (CT) scanshowed a lesion with Hounsfield unit (HU) of 13, 20 and 21 on plain, venous anddelayed phase, giving an absolute wash out of 12.5%. Biochemical tests wereconsistent with a non-functioning adrenal incidentaloma. Hence she wassubjected for right retroperitoneoscopic adrenalectomy in view of suspicious ofadrenal malignancy. However, histopathology reported as a rare adrenal cysticlymphangioma.

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