Yasemin Behram KANDEMİR, Veysel TOSUN, Necmettin KORUCUK, Ünal GÜNTEKİN

Erişkin yaşta başvuran asemptomatik parsiyel atriyoventriküler septal defekt hastası

Parsiyel atriyoventriküler septal defekt (parsiyel AVSD) konjenital kalp hastalıklarından biridir. Hastaların küçük bir kısmı ileri yaşlara kadar tanı almamış olabilir ve asemptomatik olarak erişkinliğe ulaşabilir. Bunlardan da sadece birkaçı zamanında tanı alıp cerrahi operasyon geçirmiş olmaktadır. Son bir yılda yorgunluk ve egzersiz dispnesi nedeniyle istenmiş olan rutin ekokardiyografisi ile ilk defa tanı konulan 36 yaşında parsiyel AVSD hastasını sunduk. Sağ kalp boşlukları üzerinde parsiyel AVSD’ nin uzun dönemde zararlı etkileri olmasından dolayı hastaya cerrahi operasyon önerildi ve hasta başarıyla tedavi edildi.

Asymptomatic partial atrioventricular septal defect patient admitted in adulthood

Partial atrioventricular septal defect (partial AVSD) is one of the congenital heart diseases. A small number of patientsmay be undiagnosed until older ages and reach adult life asymptomatically. Only few of those can reach adulthoodwithout timely diagnosis and surgical correction. We report a 36 years old partial AVSD case firstly diagnosed byroutine echocardiography that had fatigue and exertional dyspnea for one year. Because of partial AVSD has long termdetrimental effects on the right cardiac chambers, the patient was proposed for surgical operation and treatedsuccessfully.

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Minich LL, Atz AM, Colan SD, et al. Partial and transitional atrioventricular septal defect outcomes. Ann Thorac Surg 2010; 89:530-6.
Burke R, Horvath K, Landzberg M, et al. Longterm follow-up after surgical repair of ostium primum atrial septal defect in adults. J Am Coll Cardiol 1996; 27: 696-9.
Tandon R, Moller JH, Edwards JE. Unusual Longevity in Persistent Common Atrioventricular Canal. Circulation 1974; 50: 619-26.
Rodriguez FH, Moodie DS, Parekh DR, et al. Outcomes of hospitalization in adults in the United States with atrial septal defect, ventricular septal defect, and atrioventricular septal defect. Am J Cardiol 2011; 108:290-3.
Opotowsky AR, Siddiqi OK, Webb GD. Trends in hospitalizations for adults with congenital heart disease in the U.S. J Am Coll Cardiol 2009; 54:460-467.
Bergin ML, Warnes CA, Tajik AJ, Danielson GK. Partial atrioventricular canal defect: longterm follow-up after initial repair in patients ≥40 years old. J Am Coll Cardiol 1995; 25:1189-94.
El-Najdawi EK, Driscoll DJ, Puga FJ, et al. Operation for partial atrioventricular septal defect: a forty-year review. J Thorac Cardiovasc Surg 2000; 119:880-90.
Bowman JL, Dearani JA, Burkhart HM, et al. Should repair of partial atrioventricular septal