Santral Kor Miyopatisi Olan Bir Olguda Acil Sezaryende Anestezi Yönetimi: Olgu Sunumu

Santral kor miyopati; konjenital miyopatiler grubunda yer alan, nadir görülen herediter bir nöromüsküler bozukluktur. Santral kor miyopati; kas güçsüzlüğü, iskelet sistemi deformiteleri ve artmış malign hipertermi duyarlılığı ile karakterize olup bu hastaların anestezi yönetimi ayrı bir önem taşımaktadır. Bu hastalarda perioperatif yönetimi güçleştirebilecek uzamış kas güçsüzlüğü ve malign hipertermi en hayati risklerdir. Bu olgu sunumunda santral kor miyopati hastalığı olduğu bilinen elektif sezaryen ameliyatı planlanan ancak acil cerrahiye alınan genç bir hastadaki anestezi yönetimi paylaşılacaktır.

Anahtar Kelimeler:

Santral kor miyopati, malign hipertermi, anestezi yönetimi

Anesthesia Management of an Emergent Caesarean Section Case with the History of Central Core Myopathy: Case Report

Central core myopatyhy is a rarely seen hereditary neuromuscular disorder that is involved in congenitally myopathies group. The disease is characterized by muscular weakness, skeleton system deformities, increased malign hyperthermia sensitivity and anesthesia management is critically important. In these patients, prolonged muscular weakness and malign hyperthermia that can complicate the perioperative management are the most critical risks. In this case report, anesthesia management of an electively planned caesarean section patient, taken into emergency surgery that is also previously known to have central core myopathy diagnosis will be shared.

Keywords:

Central core myopathy, malignant hyperthermia, anesthesia management,

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Yazışma Adresi / Address for Correspondence: Dr. Çağla Bali, Başkent Üniversitesi Tıp Fakültesi Adana Uygulama ve Araştırma Merkezi Anesteziyoloji ve Reanimasyon AD. Dadaloğlu Mh. 39. Sk. No.6 01250, Yüreğir/ADANA e-mail: caglaetike@hotmail.com geliş tarihi/received :18.02.2013 kabul tarihi/accepted:25.03.2013