Emine ÇÖLGEÇEN, Kemal ÖZYURT, Murat BORLU

BEHÇET HASTALIĞINDA DERİ VE MUKOZA BELİRTİLERİ

Behçet hastalığı rekürren oral ve genital ülserler, oküler ve kutanöz lezyonlar, artrit ve vasküler tutulum ile karakterize kesin nedeni bilinmeyen multisistem inflamatuar bir hastalıktır. Tekrarlayıcı nitelikteki oral ve genital ülserler, eritema nodozum benzeri lez- yonlar ve papülopüstüler lezyonlar başta olmak üzere çeşitli deri ve mukoza bulguları gösteren hastalığın tanısında da bu bulguların kritik önemi bulunmaktadır. Ayrıca, Behçet hastalığındaki mukokutanöz bulguların diğer ciddi organ tutulumlarına göre prognostik belirleyici özellikleri olmamasına karşın, hastaların yaşam kalitesini etkiledikleri açıktır. Bu derlemede Behçet hastalığının deri ve mukoza belirtileri anlatılmaktadır.

Mucocutaneous Manifestations of Behcet s Disease

Behcet s disease is a multi-system inflammatory disorder of unknown origin, characteri- zed by recurrent oral and genital ulcerations, ocular and cutaneous lesions, arthritis and vascular disease. Various mucocutaneous manifestations consisting mainly of recurrent oral and genital ulcerations, erythema nodosum like lesions and papulopustular lesios constitute the hallmark of Behcet s disease and diagnostic criteria rely heavily on these symptoms. In addition, although the mucocutaneous manifestations are not one of the main prognostic determinants in Behcet s disease, they seem to impair the quality of life of the patients. In this review, mucocutaneous symptoms of Behcet s disease are outlined.

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