Bülent ÖZKURT, Yusuf YILDIZ, Yener SAĞLIK, Sinan BİLGİN

Primary malignant fibrous histiocytoma of bone in distal radius

Kemiğin primer malin fibröz histiyositomu (KPMFH) üst ekstremite özellikle de bilek çevresinde çok çok nadir yerleşim gösterir. Kemiğin primer malin fibröz histiyositomunun tedavisinin temelini lezyonun geniş olarak rezeksiyonu ile kemoterapi combine edilmesi oluşturur. Bu yazıda, radius alt kesiminde KPMFH tespit edilen ve ceraahi ile kemoterapi combine edilerek başarı ile tedavi edilen bir hasta sunuldu. Lezyon ekstraartiküler olarak kürete edildi. Yüz on dört aylık takip ve kontrolü sonrasında hastada hiçbir lokal nüks veya metastaza ait klinik ve radyolojik bulgu saptanmadı.

Radius alt uç yerleşimli kemiğin primer malign fibröz histiyositomu

Primary Malignant Fibrous Histiocytoma of Bone in Distal Radius A case of primary malignant fibrous histiocytoma of bone (MFH-B) located in the distal region of the radius is presented. It is very rare for primary MFH-B to be located in upper extremity particularly in wrist region. The mainstay of treatment for MFH-B is wide resection combined with chemotherapy. This report demonstrates a case of MFH-B of distal radius, treated successfully with surgery combined with chemotherapy.

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