Özlem ETHEMOĞLU UZUNKAYA, Sedat YASİN, İbrahim Fatih KARABABA, Özcan KOCATÜRK

Psikotik depresyon ve nöbet ile başvuran bir Fahr sendromu olgusu

Fahr sendromu, bilateral bazal ganglia kalsifikasyonu ile karakterize nadir görülen bir nöropsikiyatrik hastalıktır. Fahr tarafından ilk kez 1930'da bildirilmiştir. En sık görülen belirtiler ekstrapiramidal sistem bulguları olsa da, Fahr sendromu nadiren nöbet, bunama ve psikiyatrik belirtilerle de görülebilir. Tedavisi semptomatiktir. Bu yazıda, psikotik depresyon ve jeneralize tonik klonik nöbet ve ile başvuran bir Fahr sendromu olgusu sunulmuştur. (Anadolu Psikiyatri Derg 2016; 17(Êk.3):48-51).

A case of Fahr's syndrome presenting with psychotic depression and seizure

Fahr's syndrome is rarely occurring neuropsychiatric disease which is characterized by symmetric calcifications of basal ganglia. It was described for the first time by Fahr in 1930. Although, the most common symptoms are extrapyramidal system signs, Fahr syndrome might also present with seizure, dementia and psychiatric symptoms. Treatment is symptomatic. We report a case of Fahr syndrome presented by generalized tonic clonic seizure and psychotic depression. (Anatolian Journal of Psychiatry 2016; 17(Suppl.3):48-51).

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