Bilateral Cochlear Otosclerosis; Clinic and Radiologic Findings

Otosclerosis is a focal osseous dyscrasia of the temporal bone in human. It can be categorized into 2 types: Fenestral and retrofenestral/cochlear, depending on the topography of the lesions. According to the involvement of disease different symptoms might be seen such as conductive, sensorineural, or mixt type hearing loss. Altough the certain diagnosis of disease is histopathologic investigation, high resolution computed tomography (HRCT) is the gold standard imaging modality in the diagnosis of otosclerosis. In this case, Forty-one years old female patient who suffers from unilateral mixt type hearing loss in her right ear was presented. Although there was only traffic accident in the past there was no evidence of ossicle dislocation and any disease that might cause conductive hearing loss on HRCT imaging. Bilateral cochlear otosclerosis was observed on HRCT. Her right ear was thought to be affected by cochlear otosclerosis expanded to the lateral wall of the otic capsule that had been caused a mixt type hearing loss in the right and a sensorineural hearing loss in the left. We revealed incidentally fenestral and cochlear type represented in continium in her right ear.It is important to perform radiologic investigation to clarify the concomitant pathologies in hearing loss.

Keywords:

Otosclerosis Hearing Loss, High resolution computed tomography,

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1. Kanzara T, Virk JS. Diagnostic performance of high resolution computed tomography in otosclerosis. World J Clin Cases. 2017 July 16; 5(7): 286-291.
2. Bou-Assaly W, Mukherji S, Srinivasan A. Bilateral cavitary otosclerosis: A rare presentation of otosclerosis and cause of hearing loss. Clin İmaging. 2013; Nov-Dec;37(6):1116-8.
3. Lagleyre S, Sorrentino T, Calmels MN, Shin YJ, Escudé B, Deguine O, Fraysse B. Reliability of high-resolution CT scan in diagnosis of otosclerosis. Otol Neurotol. 2009; 30: 1152-1159.
4. Marx M, Lagleyre S, Escudé B, Demeslay J, Elhadi T, Deguine O, et al. Correlations between CT scan findings and hearing thresholds in otosclerosis. Acta Otolaryngol. 2011; 131: 351-357.
5. Harnsberger R, Glastonbury C, Michel M, Koch M. (2004) Diagnostic imaging: head and neck. 2nd ed. Philedelphia: Amirsys. P. 138-45.
6. Cureoglu S, Baylan MY, Paparella MM.Cochlear otosclerosis. Curr Opin Otolaryngol Head Neck Surg. 2010 Oct;18(5):357-62
7. Frisch T, Sorensen MS, Overgaard S, Bretlau P. Estimation of volume referent bone turnover in the otic capsule after sequential point labeling. Ann Otol Rhinol Laryngol. 2000 Jan; 109(1): 33-39.
8. Czerwińska G, Scierski W, Namysłowski G, Lisowska G, Misiołek M. The surgical  treatment  results  of  otosclerosis  at the Department of  Otolaryngology Silesian Medical University in Zabrze in years 2000-2010. Otolaryngol Pol. 2017 Apr 30;71(2):16-21.
9. Valvassori GE. Imaging of otosclerosis. Otolaryngol Clin North Am. 1993; 26: 359-371.
10. Swartz JD, Faerber EN, Wolfson RJ, Marlowe FI. Fenestral otosclerosis: significance of preoperative CT evaluation. Radiology. 1984; 151: 703-707.
11. Lee TC, Aviv RI, Chen JM, Nedzelski JM, Fox AJ, Symons SP. CT grading of otosclerosis. AJNR Am J Neuroradiol. 2009; 30: 1435-1439.
12. Shea JJ. The Teflon piston operation for otosclerosis. Laryngoscope. 1963; 73: 508-509.
13. Vicente Ade O, Yamashita HK, Albernaz PL, Penido Nde O. Computed tomography in the diagnosis of otosclerosis. Otolaryngol Head Neck Surg. 2006; 134: 685-692.
14. House JW,Cunningham CD. Otosclerosis. In: Flint PW, Haughey BH, Lund VJ, iparko JK, Richardson MA, Robbins KT, et al. (2010) Cummings otolaryngology head and neck surgery. 5th ed. Philedelphia, PA: Mosby-Elsevier. P. 2028-35.
15. Quesnel AM, Moonis G, Appel J, O'Malley JT, McKenna MJ, Curtin HD,  et al. Correlation of computed tomography  with  histopathology  in  otosclerosis. Otol Neurotol. 2013 Jan;34(1):22-8.