Mesut TEK, İdris AYDIN, Yasemin YUYUCU KARABULUT, Mürşide ÇEVİKOĞLU KILLI

VULVADA PARAÜRETRAL EKSTRAGASTROİNTESTİNAL STROMAL TÜMÖR; OLGU SUNUMU

ÖZET Gastrointestinal Stromal Tümörler (GİST), gastrointestinal sistem duvarı peristaltizmini düzenleyen İnterstisyel Cajal Hücreleri’nden (İCH) kaynaklandığı düşünülen mezenkimal tümörlerdir. Ekstragastrointestinal Stromal Tümörler (EGİST) daha nadir görülen, histoloji ve immünohistokimlyasal açıdan gastrointestinal stromal tümörler ile benzer ancak gastro intestinal yolak dışında oluşan tümörlerdir. Metastatik olmayan ekstragastrointestinal stromal tümörlerin cerrahi olarak çıkarılması altın standart tedavidir. Bu makalede, nadiren vulvadan köken alan ekstragastrointestinal stromal tümörlü bir olgu sunduk.

Anahtar Kelimeler:

EKSTRA GASTROİNTESTİNAL STROMAL TÜMÖR, GASTROİNTESTİNAL STROMAL TÜMÖR, PARAÜTERRAL KİTLE, VULVAR KİTLE

VULVAR PARAURETRAL EKSTRAGASTROINTESTİNAL STROMAL TUMOR; A CASE REPORT

SUMMARY Gastrointestinal Stromal Tumors (GISTs) are mesenchymal tumors that are arises from the wall of the gastrointestinal tract and is throught to originate from the Interstitial Cells of Cajal (ICC), which regulate the motility of the gastrointestinal tract. More rarely neoplasms with histology and immunohistochemistry similar to gastrointestinal stromal tumors may ocur outside the gastrointestinal tract and are so-called Extra-gastrointestinal Stromal Tumors (EGISTs). Surgical removal is the gold standard treatment for non-metastatic Extragastrointestinal stromal tumors. We reported a very rare case of ekstragastrointestinal stromal tumor arising from the vulva in this article.

Keywords:

EKSTRA GASTROINTESTINAL STROMAL TUMOR, GASTROINTESTINAL STROMAL TUMOR, PARAURETRAL MASS, VULVAR MASS,

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