Mesut TEK, İdris AYDIN, Yasemin Yuyucu KARABULUT, Mürşide Çevikoğlu KILLI

Vulvada Paraüretral Ekstra Gastrointestinal Stromal Tümör: Olgu Sunumu

Gastrointestinal Stromal Tümörler (GİST), gastrointestinal sistem duvarı peristaltizmini düzenleyen İnterstisyel Cajal Hücreleri'nden (İCH) kaynaklandığı düşünülen mezenkimal tümörlerdir. Ekstragastrointestinal Stromal Tümörler (EGİST) daha nadir görülen, histoloji ve immünohistokimlyasal açıdan gastrointestinal stromal tümörler ile benzer ancak gastro intestinal yolak dışında oluşan tümörlerdir. Metastatik olmayan ekstragastrointestinal stromal tümörlerin cerrahi olarak çıkarılması altın standart tedavidir. Bu makalede, nadiren vulvadan köken alan ekstragastrointestinal stromal tümörlü bir olgu sunduk.

Vulvada Paraüretral Ekstra Gastrointestinal Stromal Tümör: Olgu Sunumu Vulvar Parauretral Ekstragastroıntestinal Stromal Tumor; A Case Report

Gastrointestinal Stromal Tumors (GISTs) are mesenchymal tumors that are arises from the wall of the gastrointestinal tract and is throught to originate from the Interstitial Cells of Cajal (ICC), which regulate the motility of the gastrointestinal tract. More rarely neoplasms with histology and immunohistochemistry similar to gastrointestinal stromal tumors may ocur outside the gastrointestinal tract and are so-called Extra-gastrointestinal Stromal Tumors (EGISTs). Surgical removal is the gold standard treatment for non-metastatic Extragastrointestinal stromal tumors. We reported a very rare case of ekstragastrointestinal stromal tumor arising from the vulva in this article.

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