Reyhan AYAZ, İlayda LOÇLAR KARAALP, Ateş KARATEKE

Gebelikte Tanı Konulan Budd-Chiari Sendromu Takip ve Yönetimi – Olgu Sunumu

Abstract Budd-Chiari syndrome is a clinical disorder that causes congestive liver damage as a result of obstruction of hepatic venous blood flow. Many underlying factors cause thrombosis such as pregnancy, oral contraceptive use, myeleoproliferative diseases, antiphospholipid syndrome(aPL). Due to BCS is rarely seen in pregnancy, there are limited data , regarding pregnancy outcome and management during the pregnancy and postpartum period. In this case report, we describe a case of patients with BCS developed based on aPL during the pregnancy. Özet Budd-Chiari(BCS) sendromu hepatik venöz kanın kalbe ulaşım yolunda obstrüksiyonu sonucu konjesyona bağlı karaciğer hasarına sebep olan gebelikte nadir rastlanan bir klinik tablodur. Etiyolojisinde gebelik, oral kontraseptif kullanımı, myeleoproliferatif hastalıklar, antifosfolipid antikor sendromu gibi tromboza eğilim yaratan altta yatan birçok hastalık mevcuttur. BCS'li kadınlarda gebelik ve gebelik sonrası yönetim ve gebelik sonuçları hakkında yeterli veri bulunmamaktadır. Bu olgu sunumunda antifosfolipid antikor sendromu zemininde BCS gelişen gebe olgusu bildirilmiştir.

Anahtar Kelimeler:

Budd-Chiari Sendromu, Antifosfolipid Sendromu, GEBELİK

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