Ekrem GÜNER, Özdem Levent ÖZDAL, Emre ŞAM, Ayben Yentek BALKANAY, Şenol TONYALI, Halil Fırat BAYTEKİN, Didem KARAÇETİN

Nadir bir olgu: Retroperitoneal liposarkom

Retroperitoneal liposarkom (RPLS), retroperitonda ortaya çıkan yumuşak doku sarkomları arasında en yaygın olanıdır. Bu tümörler retroperitonda semptom vermemesi sebebiyle tanı anında büyük boyutlara erişirler. Primer RPLS’nin definitif tedavisi tümörün komplet cerrahi rezeksiyonudur fakat kritik anatomik organlara yakınlığı sebebiyle tümörün komplet cerrahi rezeksiyonu zordur. Aynı zamanda yüksek rekürrens oranı tedaviyi zorlaştıran önemli bir faktördür. Biz bu olgu sunumunda 20×18×19 cm çapında RPLS vakasını sunuyoruz. Karında şişlik şikayetiyle başvuran 49 yaşında erkek hastada RPLS tespit edildi. Dalak, sol böbrek ve sol sürrenal gland ile birlikte tümörün komplet cerrahi rezeksiyonu gerçekleştirilmesine rağmen rekürrens gelişti. Biz, rekürren tümöre de komplet cerahi rezeksiyon uyguladık. Hastanın 1 yıllık takibinde rekürrens gelişmedi.

Anahtar Kelimeler:

liposarkom, retroperiton, RPLS

A rare case: Retroperitoneal liposarcoma

Retroperitoneal liposarcoma (RPLS) is the most common of the soft tissue sarcomas that arise in the retroperitoneum. These tumors reach a large size by time of diagnosis due to absence of symptoms in retroperitoneum. The definitive treatment of primary RPLS is com- plete surgical resection of the tumor but due to its proximity to critical anatomical organs, complete surgical resection of the tumor is difficult. At the same time, the high recurrence rate of RPLS is an important factor that complicates treatment. In this case report, we present RPLS measuring 20×18×19 cm in diameter. RPLS was detected in a 49-year-old male patient who complained of abdominal fullness. Recurrence developed despite complete surgical resection of tumor with spleen, left kidney and left adrenal gland. We also per- formed complete resection of recurrent tumor. Recurrence did not develop on follow-up of the patient for 1 year.

Keywords:

Liposarcoma, retroperitoneum,

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