Mandibular Ramusun Ewing Sarkomu: Olgu Sunumu

Ewing sarkomları oldukça agresif tümörler olduğundan, erken tanı bu hastaların prognozu için çok önemlidir. Bu olgu sunumunun amacı, çocuk doktorları ve diş hekimleri arasında bu agresif tümörlerin klinik, radyolojik ve histopatolojik özellikleri hakkında farkındalık yaratmaktır. KBB polikliniğinden kliniğimize sevk edilen 10 yaşındaki çocuk hastanın yaklaşık 2-3 aydır devam eden boğaz ağrısı olduğu tespit edildi. Ayrıca sağ mandibular ramus bölgesinde son 15 gündür ekstraoral olarak fark edilmeye başlanan bir şişlik olduğu gözlendi. Panoramik radyografide mandibular ramusu tutan multiloküler bir lezyon görüldü. Lezyon konvansiyonel BT, MR ve ultrasonografi ile de değerlendirildi. Hastadan alınan biyopsi örneği histopatolojik olarak incelendi ve Ewing Sarkomu tanısı konularak Pediatrik Onkoloji Bölümü tarafından kemoterapi tedavisi başlandı.Nadiren mandibular bölgeyi etkileyen ewing sarkomlarının ağız içi bulguları periodontal hastalıklar, odontojenik ve perikoronal enfeksiyonlarla karışabilme olasılığı açısından her zaman göz önünde bulundurulmalıdır. Bu nedenle kesin tanı koymak için ek ve uygun radyografik incelemeler kullanılmalıdır.

Anahtar Kelimeler:

bilgisayarlı tomografi, ewing sarkoma, mandibula, panoramik radyografi, ultrason

Ewing Sarcoma of The Mandibular Ramus: Case Report

Since Ewing sarcomas are highly aggressive tumors, early diagnosis is very important for the prognosis of these patients. The aim of this case report is to raise awareness among pediatricians and dentists about the clinical, radiological and histopathological features of these aggressive tumors. A 10-year-old child patient referred to our clinic from the ENT outpatient clinic was found to have a sore throat that had been persisting for about 2-3 months. In addition, it was observed that there was an extraoral swelling in the right mandibular ramus region that had started to be noticed extraorally for the last 15 days. Panoramic radiography revealed a multilocular lesion involving the mandibular ramus. The lesion was also evaluated by conventional CT, MR and ultrasonography. The biopsy specimen obtained from the patient was examined histopathologically and diagnosed as Ewing's Sarcoma and treatment with chemotherapy was started by the Department of Pediatric Oncology.The oral findings of ewing sarcomas, which rarely affect the mandibular region, should always be considered for the possibility of confusion with periodontal diseases, odontogenic and pericoronal infections. Therefore, additional and appropriate radiographic examinations should be used to make a definitive diagnosis.

Keywords:

computed tomography, ewing sarcoma, mandible, panoramic radyography, ultrasonography,

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