Servelle-Martorell sendromunun cerrahi tedavisi

Servelle-Martorell sendromu, etyolojisi ve prognozu tam olarak bilinmemesine karşın, tutulan ekstremitenin yumuşak doku hipertrofisi ve kas-iskelet sistemi hipotrofisi ile karakterize, genellikle venöz, ancak nadiren arteriyel vasküler malformasyonudur. Genellikle vasküler malformasyonların tedavisinde cerrahi kısıtlı şartlarda uygulanmakla birlikte, komplikasyon gelişiminde kaçınılmazdır. Bu vasküler malformasyonlar sıklıkla kompresyon çorabı ve ilaçlar ile medikal olarak tedavi edilir. Bu yazıda, venöz malformasyon nedeniyle cerrahi olarak tedavi edilen 20 yaşında bir Servelle-Martorell sendromlu erkek olgu sunuldu.

Surgical treatment of Servelle-Martorell syndrome

Although the etiology and prognosis are not known precisely, Servelle-Martorell syndrome is often a venous, but rarely an arterial vascular malformation characterized by soft tissue hypertrophy and musculoskeletal hypotrophy of the affected extremity. In general, surgery is the choice in restricted conditions for the treatment of vascular malformations; however, it is unavoidable, if complications occur. These vascular malformations are often treated with medically using compression stockings and drugs. Herein, we present a 20-year-old male patient with Servelle-Martorell syndrome treated with surgically due to venous malformation.

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