Burak KAYA, Necip Sefa ÖZDEN, Arda ÖZDEMİR, Gökhan KOCAMAN, Mustafa Bülent YENİGÜN, Ayten KAYI CANGIR, Muhammed Emre Koçak, Hale KIVRAK

Göğüs duvarının nadir dev sarkomu: İndiferansiye pleomorfik sarkom

İndiferansiye pleomorfik sarkom veya daha önceki adıyla malign fibröz histiyositoma, fibroblast ve histiyositik hücrelerden kaynaklanan bir sarkom türüdür. Erişkinlerde tüm yumuşak doku sarkomları arasında en yaygın görülen sarkomdur. En sık görüldüğü yer alt ekstremite, ardından üst ekstremite ve retroperitonumdur. Göğüs duvarında nadiren görülür. Göğüs duvarındaki kitlelerin ayırıcı tanısında, cerrahi planlama açısından indiferansiye pleomorfik sarkom düşünülmelidir. Bu yazıda, sağ skapula üzerinde dev bir indiferansiye pleomorfik sarkom bulunan erkek bir olgu sunuldu.

A rare giant sarcoma of the chest wall: Undifferentiated pleomorphic sarcoma

Undifferentiated pleomorphic sarcoma or, as formerly called, malignant fibrous histiocytoma is a type of sarcoma which originates from fibroblast and histiocytic cells. It is the most common type of sarcoma among all soft tissue sarcomas in adults. Its most common site is the lower limb, followed by the upper limb and the retroperitoneum. It is rarely encountered on chest wall. In the differential diagnosis of masses on chest wall, it is important to consider undifferentiated pleomorphic sarcoma in surgical planning. In this article, we report a male case with a giant undifferentiated pleomorphic sarcoma located above the right scapula.

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