Elif Tanrıverdi, Levent Cansever, Mehmet Ali Bedirhan, Volkan Yaran, Deniz Sansar, Naciye Arda

Bronkovasküler fistüle bağlı masif hemoptizi ile seyreden Behçet hastalığı: Olgu sunumu

Otuz yedi yaşında erkek hasta günde 50 mL’lik tekrarlayan hemoptizi nedeniyle hastanemize başvurdu. Toraks bilgisayarlı tomografide hemoptiziden sorumlu herhangi bir patoloji izlenmedi. Bronkoskopide sağ alt lobun lateral duvarında mukozal infiltrasyonlar ve 2-3 mm’lik kabartılar görüldü. Şüpheli bölgede yapılan punch biyopsi sonrasında, masif kanama gelişti. Acilen sağ alt bilobektomi uygulandı. Alınan örnekte bronkovasküler fistül saptandı. Patolojik inceleme sonucu, Behçet hastalığı ile uyumlu idi. Hastaya yüksek doz steroid ve siklofosfamid tedavisi başlandı ve 18 ay süreyle azatiyoprin idame tedavisi uygulandı. Hasta üç yıldır semptomsuz olarak takip altındadır.

Behçet’s disease presenting with massive hemoptysis related to bronchovascular fistula: A case report

A 37-year-old male patient was admitted to our hospital with recurrent hemoptysis, 50 mL per day. Thoracic computed tomography showed no pathology responsible for hemoptysis. Bronchoscopy revealed mucosal infiltrations and 2 to 3-mm blotch in the lateral wall of the right lower lobe. After punch biopsy of the suspected area, massive bleeding occurred. Right lower bilobectomy was performed urgently. A bronchovascular fistula was noticed at the specimen. Pathological examination result was compatible with clinically suspected Behçet’s disease. The patient was given high-dose steroid and cyclophosphamide treatment and received azathioprine maintenance treatment for 18 months. He has been symptom-free for three-year follow-up

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