Ailesel Akdeniz ateşinin neden olduğu kardiyak tamponad: Olgu sunumu
Ailesel Akdeniz ateşi (AAA) tekrarlayan ateş, periton, sinoviya ve plevra gibi seröz zarların inflamasyonu ile karakterize, otoimmün bir hastalıktır. Hastalık sıklıkla jeneralize peritonit, plevrit veya monoartrit semptomları ile seyreder. Ailesel Akdeniz ateşine bağlı izole perikardit olguları oldukça nadirdir. Bu yazıda, AAA’nın neden olduğu yedi yıldır tekrarlayan ateş nöbetleri yakınması ile başvuran 60 yaşında erkek perikardiyal efüzyon mayi ve kardiyak tamponad olgusu sunuldu.
Cardiac tamponade caused by Familial Mediterranean fever: A case report
Familial Mediterranean fever (FMF) is an autoimmune disease characterized by recurrent fever and inflamation of serous membranes, including the peritoneum, synovia, and pleura. The disease often presents with the symptoms of generalized peritonitis, pleuritis, or monoarthritis. Familial Mediterranean fever in isolated cases of pericarditis are extremely rare. In this article, we present a 60-year-old male case with pericardial effusion and cardiac tamponade caused by FMF who was admitted after having complained of recurrent fever episodes over a period of seven years.
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- 1. Medlej-Hashim M, Loiselet J, Lefranc G, Mégarbané A. Familial Mediterranean Fever (FMF): from diagnosis to treatment. Sante 2004;14:261-6. [Abstract]
- 2. Ergüven M, Üçel R, Celebi AN, Pelit M. Ailevî Akdeniz ateşinin demografik, klinik ve genetik özellikleri ile tedaviye yanıtı: 120 vakalık tek merkez deneyimi. Çocuk Sağlığı ve Hastalıkları Dergisi 2006;49:283-90.
- 3. Dabestani A, Noble LM, Child JS, Krivokapich J, Schwabe AD. Pericardial disease in familial Mediterranean fever: an echocardiographic study. Chest 1982;81:592-5.
- 4. Zimand S, Tauber T, Hegesch T, Aladjem M. Familial Mediterranean fever presenting with massive cardiac tamponade. Clin Exp Rheumatol 1994;12:67-9.
- 5. Mangi AA, Torchiana DF. Pericardial disease. In: Cohn LH, Edmunds LH, editors. Cardiac surgery in the adult. 2nd ed. New York: The McGray-Hill Companies; 2003. p. 1359-71.
- 6. Turesson C, Jacobsson L, Bergström U. Extra-articular rheumatoid arthritis: prevalence and mortality. Rheumatology (Oxford) 1999;38:668-74.
- 7. Kees S, Langevitz P, Zemer D, Padeh S, Pras M, Livneh A. Attacks of pericarditis as a manifestation of familial Mediterranean fever (FMF). QJM 1997;90:643-7.
- 8. Tutar E, Akar N, Atalay S, Yilmaz E, Akar E, Yalçinkaya F. Familial Mediterranean fever gene (MEFV) mutations in patients with rheumatic heart disease. Heart 2002;87:568-9.
- 9. Livneh A, Langevitz P, Zemer D, Zaks N, Kees S, Lidar T, et al. Criteria for the diagnosis of familial Mediterranean fever. Arthritis Rheum 1997;40:1879-85.
- 10. Baganha MF, Pêgo A, Lima MA, Gaspar EV, Cordeiro AR. Serum and pleural adenosine deaminase. Correlation with lymphocytic populations. Chest 1990;97:605-10.