Süleyman Savaş Hacıevliyagil, Gazi Gülbaş, Levent Cem Mutlu, Özkan Yetkin, Hakkı Ulutaş, Hakan Günen

Bir Olgu Nedeniyle Poland Sendromu

Poland sendromu pektoralis major kasının tek taraflı yokluğu ile karakterize konjenital bir sendromdur. Bu sendroma meme, el ve diğer organ anomalileri de eşlik edebilir. Genellikle sağ tarafı tutar ve erkeklerde daha sıktır. Otuzaltı yaşında hemoptizi ile başvuran erkek hastanın çekilen akciğer grafisinde sağ hemitoraksta saydamlık artışı saptandı. Bu nedenle çekilen toraks bilgisayarlı tomografisinde Poland sendromu saptandı. Bu olgu az görüldüğü ve radyolojik özellikleri nedeniyle sunulmuştur. Anahtar kelimeler: Poland sendromu, Pektoralis major kası, Tek taraflı saydam akciğer. Poland Syndrome:

Anahtar Kelimeler:

Poland sendromu, Pektoralis major kası, Tek taraflı saydam akciğer. Poland Syndrome:

Poland Syndrome: A Case Report

Poland syndrome is a rarely encountered genetical disorder that is characterized with unilateral absence of pectoralis major muscle. Upper extremity deformities and anomalies in the breast, nipple and hand may accompany the syndrome. It is generally right sided and is more frequent in males. A 36 year-old male patient's PA chest X-ray who was admitted with the complaint of haemoptysis, showed rightsided hyperlucency. His chest computed tomography demonstrated Poland syndrome. This patient was presented as case report because of rarity of Poland syndrome. Key words: Poland syndrome, Absence of pectoralis major, Unilateral hyperlusensy. Poland sendromu tek taraflı pektoralis major kasının yokluğu ile karakterize konjenital

Keywords:

Poland syndrome, Absence of pectoralis major, Unilateral hyperlusensy. Poland sendromu tek taraflı pektoralis major kasının yokluğu ile karakterize konjenital,

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