Furkan Ufuk, İsmail Doğu Kılıç, Hüseyin Gökhan Yavaş, İbrahim Hasbey

Sol ventrikül nonkompaksiyonu:Manyetik rezonans görüntüleme bulguları

Sol ventrikül nonkompaksiyonu (SVNC), sol ventrikül miyokardının nadir görülen morfo-lojik bir anomalisidir. Sol ventrikül boşluğu ile komşu derin intertrabeküler oyuklar ile tra-beküle halde miyokard ile karakterizedir. Sol ventrikülün apikal ve midventriküler seg-mentleri en sık etkilenen kesimlerdir. SVNC'li hastalar asemptomatik olabileceği gibi bu hastalarda göğüs ağrısı, kalp yetmezliği ve aritmiler görülebilir. İleri hastalık aşamalarında, çoğu hastada kalp yetmezliği gelişir. Ek olarak, SVNC embolik olaylara, aritmilere ve ani ölüm gibi komplikasyonlara yol açabilir. Bu komplikasyonlar, yüksek riskli hastaların erken tanı ve zamanında tedavisi ile önlenebilir. Biz burada asemptomatik bir SVNC olgusu sunarak SVNC’nin manyetik rezonans görüntüleme bulgularını ortaya koymayı amaçladık.

Left ventricular noncompaction: Magnetic resonance imaging findings

Left ventricular noncompaction (LVNC) is a rare morphological abnormality of the left ventricular myocardium. It is characterized by trabeculated myocardium with adjacent deep intertrabecular recesses communicating with the left ventricular cavity. Most com-monly, the apical and midventricular segments of left ventricle are affected. Patients with LVNC may have no symptoms or present with chest pain, heart failure, and arrhythmias. In the advanced disease stages, heart failure is present in most of the patients. In additi-on, LVNC can lead to fatal complications, such as embolic events, arrhythmias, and sud-den death. These complications can be avoided with early diagnosis and timely treat-ment of patients at high risk. Herein, we presented an asymptomatic case of LVNC and our aim was to demonstrate the magnetic resonance imaging findings of LVNC.

PDF

___

1. Ritter M, Oechslin E, Sütsch G, Attenhofer C, Schneider J, Jenni R. Isolated noncompaction of the myocardium in adults. Mayo Clin Proc 1997;72:26-31. https://doi. org/10.1016/S0025-6196(11)64725-3
2. Weir-McCall JR, Yeap PM, Papagiorcopulo C, et al. Left ventricular noncompaction: Anatomical phenotype or distinct cardiomyopathy? J Am Coll Cardiol 2016;68:2157-2165. https://doi.org/10.1016/j. jacc.2016.08.054
3. Enríquez RA, Baeza VR, Gabrielli NL, Córdova AS, Castro GP. [Non compaction cardiomyopathy: A series of 15 cases]. Rev Med Chil 2011;139:864-871. https://doi.org/S0034-98872011000700006
4. Maheshwari M, Gokroo RK, Kaushik SK. Isolated non-compacted right ventricular myocardium. J Assoc Physicians India 2012;60:56-57.
5. Oechslin EN, Attenhofer Jost CH, Rojas JR, Kaufmann PA, Jenni R. Long-term follow-up of 34 adults with isolated left ventricular noncompaction: A distinct cardiomyopathy with poor prognosis. J Am Coll Cardiol 2000;36:493-500. https://doi.org/10.1016/S0735- 1097(00)00755-5
6. Thuny F, Jacquier A, Jop B, et al. Assessment of left ventricular non-compaction in adults: Side-byside comparison of cardiac magnetic resonance imaging with echocardiography. Arch Cardiovasc Dis 2010;103:150-159. https://doi.org/10.1016/j. acvd.2010.01.002
7. Engberding R, Stöllberger C, Ong P, Yelbuz TM, Gerecke BJ, Breithardt G. Isolated non-compaction cardiomyopathy. Dtsch Arztebl Int 2010;107:206-213. https://doi.org/10.3238/arztebl.2010.0206
8. Yousef ZR, Foley PW, Khadjooi K, et al. Left ventricular non-compaction: Clinical features and cardiovascular magnetic resonance imaging. BMC Cardiovasc Disord 2009;9:37. https://doi.org/10.1186/1471-2261-9-37
9. Ivanov A, Dabiesingh DS, Bhumireddy GP, et al. Prevalence and prognostic significance of left ventricular noncompaction in patients referred for cardiac magnetic resonance imaging. Circ Cardiovasc Imaging 2017;10:1- 10. https://doi.org/10.1161/CIRCIMAGING.117.006174
10. Zuccarino F, Vollmer I, Sanchez G, Navallas M, Pugliese F, Gayete A. Left ventricular noncompaction: Imaging findings and diagnostic criteria. AJR Am J Roentgenol 2015;204:519-530. https://doi.org/10.2214/ AJR.13.12326