Mustafa Bekir SELÇUK, Ümit BELET, Seher SAĞLAM, Türkay C. YALIN, T. Nedim KARAİSMAİLOĞLU

Sprengel deformitesi: İki kardeş olgusu

Sprengel deformitesi, skapulanın boyundaki fetal pozisyonundan toraks süperoposteriorundaki normal lokalizasyonuna, kaudal inişi sırasındaki bir bozukluk sonucu meydana gelen konjenital skapula yüksekliğidir. Sıklıkla beraberinde çeşitli anomaliler vardır. İzole bir deformite olmadığından hastanın ayrıntılı incelenmesi önemlidir. Sprengel deformitesi bulunan iki kardeş olgusu sunulmuş ve literatür gözden geçirilmiştir.

Anahtar Kelimeler:

Tanı, Kas-iskelet anomalileri, Doğumsal, kalıtsal ve yenidoğan hastalıkları ve anormallikleri, Radyografi, Skapula, Omuz eklemi

Sprengel deformity: Two sister cases

Sprengel deformity is the congenital high scapula which occurs as a result of interruption of the normal caudal migration of scapula from its fetal position in the neck to its normal position in the upper posterior thorax. Congenital high scapula is often associated with numerous anomalies. Because it is not an isolated deformity, it is vital to examine the patient carefully. We present two sister cases of Sprengel deformity with associated anomalies and review the literature.

Keywords:

Diagnosis Musculoskeletal Abnormalities, Congenital, Hereditary, and Neonatal Diseases and Abnormalities, Radiography, Scapula, Shoulder Joint,

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