Stiff Person sendromlu hastanın Gordon’un fonksiyonel sağlık örüntüleri modeli doğrultusunda öz etkililik-yeterlilik durumunun incelenmesi-olgu sunumu

Stiff Person Sendromu, kaslarda rijidite, ani myoklonik sıçrama ve spazmlar ile tonik aktiviteler şeklinde seyreden otoimmün bir hastalıktır. Hasta A.K.’nin şikayetleri sol kolda kasılma şeklinde ortaya çıkmış daha sonra sağ kol ve sırt bölgesine yayılmıştır. Kasılmalar ve hareket etmekle şiddeti artan ağrılardan rahatsız olan hasta günlük işlerini yapamayacak duruma gelmiştir. Hastanın dış merkezde yapılan tetkiklerinde Glutamik Dekarboksilaz enzim seviyesi yüksek çıkmıştır. Bu olgu sunumunda Stiff Person Sendromlu bir hastanın, Gordon’un fonksiyonel sağlık örüntüleri modelinden yararlanarak hemşirelik bakım planı sunulmuştur. Bu olguya göre; ‘’ağrı’’, ‘’uyku örüntüsünde bozulma’’, ‘’beden gereksinimden az beslenme‘’, ‘’öz bakım eksikliği’’, ‘’beden imgesinde bozulma’’, ‘’fiziksel harekette bozulma’’, ‘’fonksiyonel inkontinans’’ tanıları ele alınmış ve tanılara yönelik girişimler yapılmıştır. Sonuç olarak; bu vakayla oldukça nadir görülen Stiff Person Sendromlu bireyin sistematik ve bütüncül değerlendirilmesi ile sendroma ilişkin farkındalık oluşması ve kanıt temelli planlanan çalışmalara yol gösterici olacağı düşünülmektedir.

Anahtar Kelimeler:

Stiff person sendromu, bakım planı, hemşirelik bakımı, olgu sunumu

Investigation of self efficiency-sufficiency ın patient with stiff person syndrome according to Gordon's functional health patterns model-case report

Stiff Person Syndrome; it is an autoimmune disease that progresses in the form of rigidity in the muscles, sudden myoclonic jumps, spasms and tonic activities. The complaints of the patient A.K. appeared as a contraction in the left arm, and then spread to the right arm and back. While the patient has contractions, he also has severe pain at the same time, and he has become unable to do his daily work as the severity of the contractions increases. Glutamic Decarboxylase enzyme level was found high in the patient's external examinations. In this case report, a nursing care plan was presented by taking advantage of Gordon's functional health patterns model of a patient with Stiff Person Syndrome. According to this phenomenon; '' pain '', '' sleep pattern deterioration '', '' less-than-body nutrition '', '' lack of self-care '', '' body image deterioration '', '' physical movement deterioration '', '' functional Incontinence '' diagnoses were addressed and attempts were made to diagnose them. As a result; It is thought that systematic and holistic evaluation of Stiff Person Syndrome, which is rarely seen with this case, will raise awareness about the syndrome and guide studies that are planned based on evidence.

Keywords:

Stiff person syndrome, care plan, nursing care, case report,

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