Gülay Çiler ERDAĞ, Ayça VİTRİNEL, RAHİME GÜL YEŞİLTEPE MUTLU, YASEMİN AKIN, Semiramis SADIKOĞLU

İdyopatik pulmoner hemosiderosis tanılı olgu sunumu

Bu yazıda; hiçbir pulmoner semptomu olmadan anemiyle başvuran ve idyopatik pulmoner hemosiderosis tanısı alan 12 yaşındaki erkek olgu sunulmuştur. Hastaya daha once çok sayıda hastanede çeşitli tetkikler yapılmış ve demir eksikliği anemisi için çok sayıda kan transfüzyonu uygulanmıştı. Hasta ilk başvurusunda hematemezi ve gaitada gizli kan varlığı ile gastrointestinal kanama tanısı aldı; ancak 6 ay sonra tariflediği hemoptizi anemnezi bizi pulmoner hemosideroz olasılığına yönlendirdi. Akciğer biopsisi sonucunda alveollerde hemosiderin yüklü makrofajların görülmesiyle idyopatik pulmoner hemosiderosis tanısı koyuldu.

Idıopathic pulmonary hemosiderosis - A case report

We report a case of idiopathic pulmonary hemosiderosis (IPH) in a 12 year old boy who presented with anemia without any pulmonary symptom. He had been investigated at a number of hospitals and had received multiple blood transfusions for iron deficiency anemia. At his first admission he was misdiagnosed as gastrointestinal bleeding because of hematemesis and occult blood in feces. Six months later, history of coughing blood guided us the probability of pulmonary hemosiderosis. The diagnosis of IPH was made after a biopsy of lung showed numbers of hemosiderosin-filled macrophages in the alveoli.

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