Konus Medullaris Ependimomuna Eşlik Eden İntradural Schwannom: Olgu Sunumu

ÖzGiriş:İntradural ekstramedüller tümörler içerisinde en sık görülenlerden ikisi epandimom ve schwannomdur. Bu tümörlerin aynı anda birlikte görülmesi oldukça nadir bir durumdur. Bu birliktelik genellikle nörofibromatozis(NF) gibi sendromlarla ilişkilendirilmiştir. Olgu sunumu: 38 yaşında kadın hasta, bel ağrısı şikayeti ile başvurdu. Lomber MR’daintradural 2 adet kitle izlendi. Operasyon sonrası kitlelerden biri epandimom, diğeri schwannom olarak rapor edildi.Tartışma: Epandimom ve schwannom birlikteliği nadir görülür. Genellikle NF ileilişkilidir. Sonuç: Tümör supressör genlerde bir defekt olabileceğinden bu hastalar, diğer tümörler açısından yakın takip altına alınmalıdır.

Anahtar Kelimeler:

Spinal, Epandimom, Schwannom, Nörofibromatozis

Intradural Schwannoma Accompanying with Conus Medullaris Ependymoma: A Case Report

AbstractBackground: The most common types of intradural tumors are ependymoma andschwannomma. These are rarely seen together at the same time. This cooccurence isoften associated with a syndrome called neurofibromatosis (NF). Case presentation: A 38-years-old female patient, who complained of back pain. Oncontrast enhanced spinal MR imaging, two lesion were detected. Immunohistochemical examination showed that the first lesion was schwannoma, whereas the second lesion was myxopapillary ependymoma.Discussion:Ependymoma and schwannoma are rarely seen together at the same time,which often associated with NF.Conclussion: This cooccurence should remind genetic disorders such as neurofib-romatosis and should be investigated for other tumors.

Keywords:

Spine, Ependymoma, Schwannoma, Neurofibromatosis,

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