METİN ALKAN, MUSTAFA ARSLAN, HASAN KUTLUK PAMPAL, GÜRSEL LEVENT OKTAR, Elife TÜRKAN

Megalensefali-kapiller malformasyon sendromu ve anestezi

Megalensefali-kapiller malformasyon sendromu; makrosefali, kortikal beyin malformasyonları ve polimikrogri, beyin ve vücutta asimetrik büyüme, jeneralize veya fasiyal kapiller malformasyonlar, sindaktili/polidaktili gibi dijital anomaliler ve bağ dokusu has- talıkları ile seyretmektedir. Özellikle visseral subkutanöz-kavernöz hemanjiyomlar ve variköz genişlemeler gibi hastalığa eşlik eden patolojiler ameliyat sürecinde beklenenden daha fazla kanamaya yol açarak anestezi yönetimini komplike hale getirebilmektedir. Bu olgu sunumun da Megalensefali-Kapiller Malformasyon sendromu tanısıyla izlenen ve alt ekstremitede variköz genişlemeler nedeniy- le cerrahi uygulanan bir hastadaki anestezi deneyimimizi paylaşmayı amaçladık.

Megalencephaly-capillary malformation syndrome and anesthesia

Megalencephaly-capillary malformation syndrome is characterized with macrocephaly, cerebral cortical malformations, polymic- rogria, asymmetry of brain and whole body, generalized or facial capillary malformations, digital anomalies such as syndactyly or polydactyly and connective tissue disease. Bleeding may be more than expected in these patients because of visceral subcutaneous cavernous hemangiomas and varicose dilatations and may complicate the anesthetic management. The aim of this report is to desc- ribe the anesthetic management of a patient with Megalencephaly-capillary malformation syndrome undergoing surgery for varicose dilatations of the lower extremity.

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