Nebahat TAŞDEMİR, Yusuf TAMAM, Ertuğrul UZAR, Faysal EKİCİ, Abdullah ACAR, Alparslan ŞAHİN

Behçet hastalığına bağlı psödotümör serebride kraniyal manyetik rezonans görüntülemesinde optik sinir kılıfında sıvı artışı

Psödotümör serebri Behçet hastalığında ender görülen bir durumdur. Optik sinir kılıfında genişleme ve optik sinir etrafında subaraknoid aralıkta sıvı artışı, psödotümör serebrili hastalarda nadir gözlenen manyetik rezonans (MR) bulgularıdır. Bildiğimiz kadarıyla Behçet hastalığına bağlı psödotümör serebride bu bulgular literatürde bildirilmemiştir. Bu tür olgularda lumboperitoneal şant cerrahisi medikal tedaviye yanıt alınamadığında ve görme semptomları varlığında uygulanabilmektedir. Bu yazıda, ilgili radyolojik ve klinik bulgular tartışıldı ve tedavi yöntemleri kısaca gözden geçirilmiştir.

Pseudotumor cerebri due to Behçet's disease increased fluid in the perioptic nerve sheath on cranial magnetic resonance imaging

Pseudotumor cerebri is a rare condition of Behçet’s disease. Enlargement of optic nerve sheath and increased subarachnoid fluid around the optic nerve are uncommon magnetic resonance (MR) findings of the patients with pseudotumor cerebri. To the best of our knowledge, these findings were not reported in pseudotumor cerebri due to Behçet’s disease. Lumboperitoneal shunting surgery may be performed in cases which have visual symptoms and refractory to the medical treatment. In this paper, the relevant clinical and radiological findings were discussed, and a brief overview of therapeutic management was provided.

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