Intestinal perforation in Hirschsprung's disease: a report of three cases

Hirschsprung hastalığı, yenidoğan döneminde bağırsak tıkanıklığının en önemli nedenlerinden biridir. Hirschsprung hastalığının önemli kompLikasyonu tıkanıklık ile birilikte olan bağırsak perforasyonudur. Bu yazıda bağırsak perforasyonu ile bulgu veren Hirschsprung hastalığı olan üç olguyu sunmayı, bu durumun patogenezini tartışmayı amaçladık.

Hirschsprung hastalığında bağırsak perforasyonu: Üç olgu sunumu

Hirschsprung's disease is a common cause of intestinal obstruction in the newborn period. An important complication of Hirschsprung's disease is perforation of the bowel associated with obstruction. Herein, we report three consecutive newborns with Hirschsprung's disease presenting with intestinal perforation, and discuss its pathogenesis

___

  • 1.Lall A, Gupta DK, Bajpai M. Neonatal Hirschsprung's disease. Indi­an J Pediatr 2000; 67: 583-588.
  • 2.Sarioglu A, Tanyel FC, Buyukpamukcu N, Hicsonmez A. Appendiceal­ perforation: a potentially lethal initial mode of presentation of Hirschsprung's disease. J Pediatr Surg 1997; 32: 123-124.
  • 3.Newman B, Nussbaum A, Kirkpatrick JA Jr. Bowel perforation in Hirschsprung's disease. AJR Am J Roentgenol 1987; 148: 1195-1197.
  • 4.Arliss J, Holgersen LO. Neonatal appendiceal perforation and Hirschsprung's disease. J Pediatr Surg 1990; 25: 694-695.
  • 5.Teitebaum DH, Coran AG, Weitzman JJ, Ziegler MM, Kane T. Hirschsprung's Disease and Related Neuromuscular Disorders of the Intestine. In. O'Neill JA, Rowe MI, Grosfeld JL, Fonkalsrud E W, Coran AG (eds): Pediatric surgery. 5th ed. Missouri: Mosby-Year Book Inc; 1998. p. 1381-1418.
  • 6.Newman B, Nussbaum A, Kirkpatrick JA Jr, Colodny A. Appendi­ceal perforation, pneumoperitoneum, and Hirschsprung's disease. J Pediatr Surg 1988; 23: 854-856.
  • 7.Managoli S, Chaturvedi P, Vilhekar KY, Gupta D, Ghosh S. Perfora­ted acute appendicitis in a term neonate. Indian J Pediatr 2004; 71:357-358.
  • 8.Das Narla L, Hingsbergen EA. Case 22: total colonic aganglionosislong-segment Hirschsprung disease. Radiology 2000; 215: 391-394.